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Hypoplastic Left Heart Syndrome with Congenital Complete Heart Block

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Abstract

Congenital complete atrioventricular block (CCAVB) is a rare condition with an incidence of 1 of 20,000 live births. Hypoplastic left heart syndrome (HLHS) occurs more frequently than CCAVB and occurs in 1 of 5000 live births. HLHS in association with CCAVB is exceedingly rare. In this report, we describe a rare case of HLHS and CCAVB diagnosed in utero. Postnatal diagnosis, management and outcome are presented as well as review of the medical literature.

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Authors and Affiliations

  1. Rush University Medical Center, Rush Center for Congenital Heart Disease, 1653 W. Congress Pkwy, Pavilion Building, Suite 654, Chicago, IL, USA

    Maytham Al-kubaisi, Safwat A. Aly, Bassel Mohammad Nijres & Sawsan Awad

Authors
  1. Maytham Al-kubaisi
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  2. Safwat A. Aly
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  3. Bassel Mohammad Nijres
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  4. Sawsan Awad
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Corresponding author

Correspondence to Maytham Al-kubaisi.

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The authors declare that they have no conflicts of interest related to this report.

Ethical Approval

As this is a case report, this article does not contain any studies with human participants or animals performed by any of the authors.

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Informed consent was obtained prior to all clinical procedures in accordance with standard clinical practice.

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Al-kubaisi, M., Aly, S.A., Mohammad Nijres, B. et al. Hypoplastic Left Heart Syndrome with Congenital Complete Heart Block. Pediatr Cardiol 38, 1305–1308 (2017). https://doi.org/10.1007/s00246-017-1631-8

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  • DOI: https://doi.org/10.1007/s00246-017-1631-8

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