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Right Subclavian Artery Aneurysm in an Adolescent With a Bicuspid Aortic Valve

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Abstract

Bicuspic aortic valve is the most common congenital cardiac anomaly (Fedak et al. 106:900–904, 2002), and it is associated with other structural anomalies of the aorta, such as coarctation, suggesting a common embryologic developmental mechanism (Mergan et al. 104:118–119, 2004). In more than a half of patients, it is associated with progressive dilation and aneurysm formation of the aorta (Warnes 89:965–966, 2003) despite normally functioning bicuspid aortic valves. In this context, aneurysms of the right subclavian artery are extremely rare, and even more so when associated with a right-sided aortic arch that has a left aberrant subclavian artery with a Kommerell diverticulum, as found in the reported case. These aneurysms represent a significant risk for thromboembolism and rupture, and elective surgical management should be advised, even for asymptomatic cases.

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Authors and Affiliations

  1. Department of Pediatric Cardiology, Hospital Pediátrico Carmona da Mota, Av. Afonso Romão, Santo António dos Olivais, 3000-602, Coimbra, Portugal

    J. Marinho, A. Pires, G. Sousa & E. Castela

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  1. J. Marinho
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  2. A. Pires
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  3. G. Sousa
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  4. E. Castela
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Correspondence to A. Pires.

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Marinho, J., Pires, A., Sousa, G. et al. Right Subclavian Artery Aneurysm in an Adolescent With a Bicuspid Aortic Valve. Pediatr Cardiol 34, 1952–1954 (2013). https://doi.org/10.1007/s00246-012-0502-6

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  • DOI: https://doi.org/10.1007/s00246-012-0502-6

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