Pediatric Cardiology

, Volume 34, Issue 1, pp 194–197 | Cite as

Hemangioendothelioma: A Rare Case of a Primary Intracardiac Tumor

  • Andrea BeatonEmail author
  • Trevor Kuttler
  • Ali Hassan
  • Dilip S. Nath
  • Christine Reyes
  • Richard A. Jonas
  • Gerard R. Martin
Case Report


Kaposiform hemangioendothelioma (KH) is a rare tumor of vascular origin that commonly affects the cutaneous tissues of the extremities. It can, however, affect the abdomen, thorax, head, or neck. Compared with juvenile hemangiomas, which tend to regress, KH tumors are locally aggressive and usually persist. Associated morbidity and mortality rates range from 12 to 30 % and typically are related to either compressive effects on surrounding vital structures or effects of the Kasabach–Merritt phenomenon [10, 11, 13]. To our knowledge, this report is the first to describe KH presenting as a primary intracardiac tumor.


Pediatric cardiology Cardiac tumor Pericardial effusion 


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Copyright information

© Springer Science+Business Media, LLC 2012

Authors and Affiliations

  • Andrea Beaton
    • 1
    Email author
  • Trevor Kuttler
    • 2
  • Ali Hassan
    • 3
  • Dilip S. Nath
    • 1
  • Christine Reyes
    • 1
  • Richard A. Jonas
    • 1
  • Gerard R. Martin
    • 1
  1. 1.Children’s National Medical CenterWashingtonUSA
  2. 2.Walter Reed National Military Medical CenterBethesdaUSA
  3. 3.Chest Disease HospitalKuwait CityKuwait

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