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Percutaneous Recanalization of an Occluded Hepatic Vein in a Difficult Subset of Pediatric Budd-Chiari Syndrome

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Abstract

We present a 3-year-old child with Budd Chiari syndrome having idiopathic complete occlusion of all three major hepatic veins and small hepatic venules. Adequate antegrade flow in right hepatic vein was established by transfemoral balloon angioplasty followed by stenting of the same. Long term antiplatelet therapy was instituted. Medium term follow up reveals satisfactory antegrade flow and regression of symptoms. This strategy highlights an effective nonsurgical approach of restoring physiological pattern of hepatic sinusoidal blood flow in Budd Chiari syndrome.

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Authors and Affiliations

  1. Department of Pediatric Cardiology, Manipal Hospitals, 98, HAL Airport Road, Bangalore, 560 017, India

    Maitri Chaudhuri, Mahimarangaiah Jayaranganath & Vidhyashankar Subash Chandra

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  1. Maitri Chaudhuri
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  2. Mahimarangaiah Jayaranganath
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  3. Vidhyashankar Subash Chandra
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Correspondence to Maitri Chaudhuri.

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Chaudhuri, M., Jayaranganath, M. & Chandra, V.S. Percutaneous Recanalization of an Occluded Hepatic Vein in a Difficult Subset of Pediatric Budd-Chiari Syndrome. Pediatr Cardiol 33, 806–810 (2012). https://doi.org/10.1007/s00246-012-0188-9

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  • DOI: https://doi.org/10.1007/s00246-012-0188-9

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