Abstract
Cor triatriatum sinister is an uncommon congenital cardiac defect that has rarely been described in association with left-sided partial anomalous pulmonary venous return. We present a case of such rare anatomy with multilevel obstruction that presented in infancy as cardiogenic shock. The patient underwent staged treatment with extracorporeal membrane oxygenation stabilization, catheter-based balloon dilatation of the cor triatriatum and atrial septostomy, followed by definitive surgical repair, with excellent result.
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References
Camilleri L, Lusson JR, Picarelli D, d’Agrosa MC, Peycelon B, de Riberolles C (1991) Association of cor triatriatum and obstruction of abnormal left pulmonary venous drainage. Apropos of a case. Arch Mal Coeur Vaiss 84(3):409–412
Cooley DA, Murphy MC (1990) Cor triatriatum and anomalous pulmonary venous return: An unusual case. Tex Heart Inst J 17(2):118–121
Fujimatsu T, Tsunemoto M, Shimada M, Ohta Y, Endo S, Ishizawa A et al (1990) Subtotal cor triatrium with left partial anomalous pulmonary venous connection—Successful correction in an infant. Rinsho Kyobu Geka 10(1):76–80
Geggel RL, Fulton DR, Chernoff HL, Cleveland R, Hougen TJ (1987) Cor triatriatum associated with partial anomalous pulmonary venous connection to the coronary sinus: echocardiographic and angiocardiographic features. Pediatr Cardiol 8(4):279–283
Geva T, Van Praagh S (1995) Abnormal pulmonary venous connections. In: Allen HD, Driscoll DJ, Shaddy RE, Feltes TF (eds) Heart disease in infants, children, and adolescents, 5th edn. Williams & Wilkins, Baltimore, pp 761–792
Jegier W, Gibbons GJ, Wiglesworth FW (1963) Cortriatriatum: clinical, hemodynamic and pathological studies surgical correction in early life. Pediatrics 31:255–267
Jennings RB Jr, Innes BJ (1977) Subtotal cor triatriatum with left partial anomalous pulmonary venous return. Successful surgical repair in an infant. J Thorac Cardiovasc Surg 74(3):461–466
Krasemann Z, Scheld HH, Tjan TD, Krasemann T (2007) Cor triatriatum: short review of the literature upon ten new cases. Herz 32(6):506–510
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A subcostal long-axis echocardiographic clip shows a large, tense cor chamber in the left atrium; a compressed true left atrium; a dilated right ventricle; and an underfilled left ventricle. Left-ventricular diastolic compression is indicative of right-ventricular volume overload. (AVI 5453 kb)
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A subcostal color echocardiographic clip shows increased right superior vena cava flow (red jet at the left side of the color box), right-to-left atrial level shunting (blue jet), and flow from the cor chamber to the true left atrium (red jet at the center of the color box). (AVI 2246 kb)
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Right lower pulmonary vein angiography shows drainage of the right pulmonary veins into a large, tense cor chamber with little blood egress to the left ventricle. The true left atrium is compressed by the cor chamber. (AVI 2440 kb)
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Right lower pulmonary vein angiography after balloon dilation of the cor membrane orifice. The cor chamber is smaller, there is less compression of the true left atrium, and blood flow to the left ventricle is significantly increased. (AVI 1966 kb)
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Schiller, O., Burns, K.M., Sinha, P. et al. Cor Triatriatum With Partial Anomalous Pulmonary Venous Return: A Rare Case of Parallel Obstruction and Successful Staged Treatment. Pediatr Cardiol 33, 363–365 (2012). https://doi.org/10.1007/s00246-011-0148-9
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DOI: https://doi.org/10.1007/s00246-011-0148-9