Abstract
A fetus had a diagnosis of a vascular ring formed by a right aortic arch with an aberrant left subclavian artery. The infant experienced isolated dysphagia and vomiting 3 months after birth. Magnetic resonance imaging (MRI) confirmed the vascular ring and demonstrated profound, isolated esophageal dilation with normal airways. The severity of postnatal symptoms due to a vascular ring is difficult to determine in utero. Expectant management of the lesion is necessary, and use of MRI as the imaging method allows for both confirmation of the diagnosis and evaluation of the airway and esophagus while avoiding radiation.
References
Backer CL, Hillman N, Mavroudis C, Holinger LD (2002) Resection of Kommerell’s diverticulum and left subclavian artery transfer for recurrent symptoms after vascular ring division. Eur J Cardiothorac Surg 22:64–69
Cina CS, Althani H, Pasenau J, Abouzahr L (2004) Kommerell’s diverticulum and right-sided aortic arch: a cohort study and review of the literature. J Vasc Surg 39:131–139
Humphrey C, Duncan K, Fletcher S (2006) Decade of experience with vascular rings at a single institution. Pediatrics 117:e903–e908
Juraszek AL, Guleserian KJ (2006) Common aortic arch anomalies: diagnosis and management. Curr Treat Options Cardiovasc Med 8:414–418
Kocis KC, Midgley FM, Ruckman RN (1997) Aortic arch complex anomalies: 20-year experience with symptoms, diagnosis, associated cardiac defects, and surgical repair. Pediatr Cardiol 18:127–132
Li S, Luo G, Norwitz E, Wang C, Chen X, Bi J (2011) Prenatal diagnosis of congenital vascular rings and slings: sonographic features and perinatal outcome in 81 consecutive cases. Prenat Diag 31:334–346
Marmon LM, Bye MR, Haas JM, Balsara RK, Dunn JM (1984) Vascular rings and slings: long-term follow-up of pulmonary function. J Pediatr Surg 19:683–692
Patel CR, Lane JR, Spector ML, Smith PC (2006) Fetal echocardiographic diagnosis of vascular rings. J Ultrasound Med 25:251–257
Tuo G, Volpe P, Bava GL, Bondanza S, De Robertis V, Pongiglione G, Marasini M (2009) Prenatal diagnosis and outcome of isolated vascular rings. Am J Cardiol 103:416–419
Turner A, Gavel G, Coutts J (2005) Vascular rings: presentation, investigation and outcome. Eur J Pediatr 164:266–270
Woods RK, Sharp RJ, Holcomb GW III, Snyder CL, Lofland GK, Ashcraft KW, Holder TM (2001) Vascular anomalies and tracheoesophageal compression: a single institution’s 25-year experience. Ann Thorac Surg 72:434–438 discussion 438–439
Yoo SJ, Min JY, Lee YH, Roman K, Jaeggi E, Smallhorn J (2003) Fetal sonographic diagnosis of aortic arch anomalies. Ultrasound Obstet Gynecol 22:535–546
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Olivieri, L.J., Cross, R.R. & Donofrio, M.T. Influence of Fetal Diagnosis on the Clinical Presentation of a Vascular Ring. Pediatr Cardiol 33, 351–353 (2012). https://doi.org/10.1007/s00246-011-0129-z
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DOI: https://doi.org/10.1007/s00246-011-0129-z