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Hypoplastic Left Heart Syndrome, Restrictive Patent Foramen Ovale, and Pulmonary Valve Stenosis: An Unusual Combination

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Abstract

An infant presented with a rare combination of hypoplastic left heart syndrome, restricted patent foramen ovale, and moderately dysplastic pulmonary valve. In preparation for heart transplantation, bilateral pulmonary artery banding was performed to protect the pulmonary vasculature.

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References

  1. Abbag FI, Alhayani AA, Moussa HA, Al-Qahtani JM, Al-Barki AA (2007) Hypoplastic left heart syndrome and valvular pulmonary stenosis: a rare association that limits the management options. Saudi Med J 28:620–622

    PubMed  Google Scholar 

  2. Bharati S, Nordenberg A, Brock RR, Lev M (1984) Hypoplastic left heart syndrome with dysplastic pulmonary valve with stenosis. Pediatr Cardiol 5:127–130

    Article  PubMed  CAS  Google Scholar 

  3. Canter CE, Moorehead S, Huddleston CB, Spray TL (1993) Restrictive atrial septal communication as a determinant of outcome of cardiac transplantation for hypoplastic left heart syndrome. Circulation 88:II456–II460

    PubMed  CAS  Google Scholar 

  4. Farra H, Kort HW (2005) Hypoplastic left heart syndrome and valvar pulmonary stenosis: presentation and management. Pediatr Cardiol 26:680–682

    Article  PubMed  CAS  Google Scholar 

  5. Glatz JA, Tabbutt S, Gaynor JW, Rome JJ, Montenegro L et al (2007) Hypoplastic left heart syndrome with atrial level restriction in the era of prenatal diagnosis. Ann Thorac Surg 84:1633–1638

    Article  PubMed  Google Scholar 

  6. Noonan JA, Nadas AS (1958) The hypoplastic left heart syndrome: an analysis of 101 cases. Pediatr Clin North Am 5:1029–1056

    PubMed  CAS  Google Scholar 

  7. Rychik J, Rome JJ, Collins MH, DeCampli WM, Spray TL (1999) The hypoplastic left heart syndrome with intact atrial septum: atrial morphology, pulmonary vascular histopathology, and outcome. J Am Coll Cardiol 34:554–560

    Article  PubMed  CAS  Google Scholar 

  8. Vlahos AP, Lock JE, McElhinney DB, van der Velde ME (2004) Hypoplastic left heart syndrome with intact or highly restrictive atrial septum: outcome after neonatal transcatheter atrial septostomy. Circulation 109:2326–2330

    Article  PubMed  Google Scholar 

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Correspondence to Sanjeev Aggarwal.

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246_2011_119_MOESM1_ESM.avi

Movie 1 Apical four-chamber view showing a severely hypoplastic left ventricle, mild mitral regurgitation, and trivial tricuspid regurgitation. (AVI 2060 kb)

Movie 2 Subcostal view showing a severely restricted patent foramen ovale. (AVI 1723 kb)

Movie 3 Parasteral short-axis view demonstrating a moderately dysplastic pulmonary valve. (AVI 2448 kb)

Movie 4 High parastenal axis view showing the bilateral pulmonary artery bands. (AVI 2114 kb)

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Aggarwal, S., Delius, R.E., Walters, H.L. et al. Hypoplastic Left Heart Syndrome, Restrictive Patent Foramen Ovale, and Pulmonary Valve Stenosis: An Unusual Combination. Pediatr Cardiol 33, 357–359 (2012). https://doi.org/10.1007/s00246-011-0119-1

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  • DOI: https://doi.org/10.1007/s00246-011-0119-1

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