Pediatric Cardiology

, 32:1048 | Cite as

Intrapericardial and Retrocardial Implantation of Implantable Cardioverter-Defibrillator Lead in a Child with Type 3 Long QT Syndrome

  • Yasuhiro Ichikawa
  • Mari IwamotoEmail author
  • Sadamitsu Yanagi
  • Munetaka Masuda
Case Report


A 6-year-old girl with type 3 long QT syndrome was safely and successfully implanted with an implantable cardioverter-defibrillator (ICD) system. Prior to implantation, she had experienced uncontrollable life-threatening arrhythmia in spite of high-dose administration of mexiletine. An ICD coil lead for transvenous use was placed in the intrapericardial and retrocardial space and was connected to a generator placed in front of the posterior sheath of the right abdominal rectal muscle. Administration of a beta-blocker in addition to atrial pacing almost completely eliminated the patient’s life-threatening arrhythmia attacks. Intrapericardial and retrocardial implantation of ICD coil leads might be useful for children.


Implantable cardioverter-defibrillator LQT3 Beta-blocker Mexiletine Intrapericardial and retrocardial approach Child 


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Copyright information

© Springer Science+Business Media, LLC 2011

Authors and Affiliations

  • Yasuhiro Ichikawa
    • 1
  • Mari Iwamoto
    • 1
    Email author
  • Sadamitsu Yanagi
    • 2
  • Munetaka Masuda
    • 3
  1. 1.Department of Pediatric CardiologyYokohama City UniversityYokohama CityJapan
  2. 2.Department of Pediatric CardiologyKanagawa Children’s Medical CenterYokohama CityJapan
  3. 3.Department of Cardiac SurgeryYokohama City UniversityYokohama CityJapan

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