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Ductal Origin of the Pulmonary Artery in Isolation: A Case Series

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Abstract

We present three cases of ductal origin of a pulmonary artery in the absence of associated structural heart disease. No geographic or genetic explanation for the temporal occurrence of these cases could be identified. This series illustrates the importance of angiography in achieving an accurate diagnosis as well as appropriate surgical planning. An understanding of the embryologic origin of this lesion supports the strategic approach at catheterization as well as the surgical choice of interposition graft versus direct anastomosis. We report our experience and highlight diagnostic and surgical approaches to such patients based on the underlying embryology of this congenital cardiac anomaly.

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Authors and Affiliations

  1. Department of Internal Medicine–Pediatrics, Maine Medical Center–Barbara Bush Children’s Hospital, Portland, ME, 04103, USA

    Daniel Cox

  2. Department of Cardiothoracic Surgery, Maine Medical Center–Barbara Bush Children’s Hospital, Portland, ME, 04103, USA

    Reed Quinn

  3. Department of Pediatric Cardiology, Maine Medical Center–Barbara Bush Children’s Hospital, Portland, ME, 04103, USA

    Adrian Moran & Jon Donnelly

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  1. Daniel Cox
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  2. Reed Quinn
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  3. Adrian Moran
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  4. Jon Donnelly
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Correspondence to Daniel Cox.

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Cox, D., Quinn, R., Moran, A. et al. Ductal Origin of the Pulmonary Artery in Isolation: A Case Series. Pediatr Cardiol 31, 997–1001 (2010). https://doi.org/10.1007/s00246-010-9744-3

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  • DOI: https://doi.org/10.1007/s00246-010-9744-3

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