Abstract
Scimitar syndrome is a rare cause of left-to-right shunting. Surgery is indicated for a pulmonary-to-systemic blood flow ratio greater than 1.5:1 and not infrequently is complicated by postoperative obstruction. This report presents a case of scimitar syndrome and reviews how magnetic resonance imaging (MRI) can be used for initial and follow-up assessment of the syndrome with emphasis on suspected pulmonary venous obstruction. Given the potential high incidence of postoperative occlusion, MRI provides hemodynamic and anatomic information for both initial and follow-up assessment of scimitar syndrome. MRI clearly demonstrated transpleural pulmonary-to-systemic venous collaterals draining the obstructed scimitar vein.
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Alsoufi B, Cai S, Van Arsdell GS, Williams WG, Caldarone CA, Coles JG (2007) Outcomes after surgical treatment of children with partial anomalous pulmonary venous connection. Ann Thorac Surg 84:2020–2026
Brown JW, Ruzmetov M, Minnich DJ, Vijay P, Edwards CA, Uhlig PN, Fiore AC, Turrentine MW (2003) Surgical management of scimitar syndrome: an alternative approach. J Thorac Cardiovasc Surg 125:238–245
Dupuis C, Charaf LA, Abou CP, Breviere GM (1993) Surgical treatment of the scimitar syndrome in children, adolescents, and adults: a cooperative study of 37 cases. Arch Mal Coeur Vaiss 86:541–547
Gavazzi E, Ravanelli M, Farina D, Chiari ME, Maroldi R (2008) Scimitar syndrome: comprehensive, noninvasive assessment with cardiovascular magnetic resonance imaging. Circulation 118:e63–e64
Grosse-Wortmann L, Al Otay A, Goo HW, Macgowan CK, Coles JG, Benson LN, Redington AN, Yoo SJ (2007) Anatomical and functional evaluation of pulmonary veins in children by magnetic resonance imaging. J Am Coll Cardiol 49:993–1002
Khan MA, Torres AJ, Printz BF, Prakash A (2005) Usefulness of magnetic resonance angiography for diagnosis of scimitar syndrome in early infancy. Am J Cardiol 96:1313–1316
Najm HK, Williams WG, Coles JG, Rebeyka IM, Freedom RM (1996) Scimitar syndrome: twenty years’ experience and results of repair. J Thorac Cardiovasc Surg 112:1161–1168
Roman KS, Kellenberger CJ, Macgowan CK, Coles J, Redington AN, Benson LN, Yoo SJ (2005) How is pulmonary arterial blood flow affected by pulmonary venous obstruction in children? A phase-contrast magnetic resonance study. Pediatr Radiol 35:580–586
Wiebe S, Maclusky I, Manson D, Holowka S, Yoo SJ (2003) Hemoptysis: a rare cause can be related to a bronchial varix due to pulmonary venous obstruction. Pediatr Radiol 33:884–886
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Wong, D.T.H., Grosse-Wortmann, L. & Yoo, SJ. Transpleural Pulmonary-to-Systemic Venous Collaterals in a Case With Obstructed Scimitar Vein. Pediatr Cardiol 31, 1086–1088 (2010). https://doi.org/10.1007/s00246-010-9741-6
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DOI: https://doi.org/10.1007/s00246-010-9741-6