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Successful Staged Neonatal Repair of Tetralogy of Fallot with Long-Segment Hypoplasia of the Aorta

Pediatric Cardiology volume 31, pages 124–127 (2010)Cite this article

Abstract

We describe an extremely rare combination of tetralogy of Fallot (TOF), right-sided cervical aortic arch with long-segment hypoplasia, and other vascular anomalies. A two-stage surgical approach included aortic arch reconstruction followed by right ventricular muscle bundle division and ventricular septal defect closure a few weeks later. The initial clinical presentation, perioperative course, and imaging studies are presented along with a review of the relevant literature. This is the first report of successful neonatal repair of TOF with long-segment hypoplasia of the aorta.

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Authors and Affiliations

  1. Congenital Heart Center, University of Michigan, Ann Arbor, MI, 48109-5204, USA

    Jimmy C. Lu, Sanket S. Shah, Sonal T. Owens, Adam L. Dorfman, Ameeth Vedre, Monica M. Goble, Jennifer C. Hirsch & John R. Charpie

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  1. Jimmy C. Lu
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  2. Sanket S. Shah
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  3. Sonal T. Owens
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  4. Adam L. Dorfman
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  5. Ameeth Vedre
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  6. Monica M. Goble
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  7. Jennifer C. Hirsch
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  8. John R. Charpie
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Correspondence to Jimmy C. Lu.

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Jimmy C. Lu and Sanket S. Shah contributed equally to this work.

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Lu, J.C., Shah, S.S., Owens, S.T. et al. Successful Staged Neonatal Repair of Tetralogy of Fallot with Long-Segment Hypoplasia of the Aorta. Pediatr Cardiol 31, 124–127 (2010). https://doi.org/10.1007/s00246-009-9547-6

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  • DOI: https://doi.org/10.1007/s00246-009-9547-6

Keywords

  • Aortic arch hypoplasia
  • Coarctation
  • Interrupted aortic arch
  • Neonatal repair
  • Tetralogy of Fallot