We describe an extremely rare combination of tetralogy of Fallot (TOF), right-sided cervical aortic arch with long-segment hypoplasia, and other vascular anomalies. A two-stage surgical approach included aortic arch reconstruction followed by right ventricular muscle bundle division and ventricular septal defect closure a few weeks later. The initial clinical presentation, perioperative course, and imaging studies are presented along with a review of the relevant literature. This is the first report of successful neonatal repair of TOF with long-segment hypoplasia of the aorta.
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Jimmy C. Lu and Sanket S. Shah contributed equally to this work.
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Lu, J.C., Shah, S.S., Owens, S.T. et al. Successful Staged Neonatal Repair of Tetralogy of Fallot with Long-Segment Hypoplasia of the Aorta. Pediatr Cardiol 31, 124–127 (2010). https://doi.org/10.1007/s00246-009-9547-6
- Aortic arch hypoplasia
- Interrupted aortic arch
- Neonatal repair
- Tetralogy of Fallot