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Fatal Cardiac Arrest Due to an Unusual Fibroma of the Pulmonary Valve

Pediatric Cardiology volume 30, pages 536–539 (2009)Cite this article

Abstract

Fibroma, the second most common tumor in childhood, usually is a large solitary mass involving the ventricular septum or the left and rarely the right free ventricular wall. An unusual case of a 5.2-year-old boy with a large mass originating from the pulmonary valve is reported. The patient presented for evaluation of a murmur. Echocardiography and cardiac magnetic resonance imaging showed a large tumor extending from the distal right ventricular outflow tract through the pulmonary valve and into the main pulmonary artery causing moderate obstruction. The patient had a fatal cardiac arrest while awaiting surgery. The postmortem examination proved the tumor to be a fibroma.

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Affiliations

  1. Pediatric Cardiology Department, Onassis Cardiac Surgery Center, Athens, Greece

    Maria G. Kiaffas & Spyridon Rammos

  2. Hygeia Hospital, Cardiac Magnetic Resonance Center, Athens, Greece

    Peter G. Danias

  3. Tufts University School of Medicine, Boston, MA, USA

    Peter G. Danias

  4. Pathology Department, Onassis Cardiac Surgery Center, Athens, Greece

    Loukas Kaklamanis

Authors
  1. Maria G. Kiaffas
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  2. Peter G. Danias
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  3. Loukas Kaklamanis
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  4. Spyridon Rammos
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Corresponding author

Correspondence to Maria G. Kiaffas.

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Kiaffas, M.G., Danias, P.G., Kaklamanis, L. et al. Fatal Cardiac Arrest Due to an Unusual Fibroma of the Pulmonary Valve. Pediatr Cardiol 30, 536–539 (2009). https://doi.org/10.1007/s00246-008-9380-3

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  • DOI: https://doi.org/10.1007/s00246-008-9380-3

Keywords

  • Cardiac MRI
  • Pediatric cardiac fibroma
  • Pulmonary valve