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Chronic Granulomatous Disease Associated with Atypical Kawasaki Disease

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Abstract

Chronic granulomatous disease (CGD) is an infrequent inherited disorder characterized by recurrent infections and abnormal granuloma formation. Patients with CGD have an exuberant inflammatory response and an increased risk of developing autoimmunity. We present the case of a 1-year-old boy with CGD who developed several of the characteristic clinical features of Kawasaki Disease. His illness responded to intravenous immunoglobulin, aspirin, and corticosteroids.

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Acknowledgments

The authors thank S. Nayak and S. Nayak for technical assistance and helpful discussions.

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Authors and Affiliations

  1. Department of Clinical Immunology, Instituto Nacional de Pediatría, Insurgentes Sur 3700-C C.P, 04530, Col. Insurgentes Cuicuilco, Mexico City, Mexico

    M. A. Yamazaki-Nakashimada & N. Ramírez-Vargas

  2. Department of Cardiology, Instituto Nacional de Pediatría, Mexico City, Mexico

    J. De Rubens-Figueroa

Authors
  1. M. A. Yamazaki-Nakashimada
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  2. N. Ramírez-Vargas
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  3. J. De Rubens-Figueroa
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Correspondence to M. A. Yamazaki-Nakashimada.

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Yamazaki-Nakashimada, M.A., Ramírez-Vargas, N. & De Rubens-Figueroa, J. Chronic Granulomatous Disease Associated with Atypical Kawasaki Disease. Pediatr Cardiol 29, 169–171 (2008). https://doi.org/10.1007/s00246-007-9011-4

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  • DOI: https://doi.org/10.1007/s00246-007-9011-4

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