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Pulmonary Atresia with Intact Ventricular Septum Coexisting with Coarctation of the Aorta

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Abstract

A newborn with pulmonary atresia, intact ventricular septum, and a bicommissural aortic valve underwent percutaneous pulmonary valvotomy at 1 day of age. Severe coarctation of the aorta became apparent only after spontaneous closure of the ductus arteriosus at 5 weeks of age, requiring repair by surgical end-to-end anastomosis. This is the first report of a child with pulmonary atresia with intact ventricular septum in association with coarctation of the aorta.

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Authors and Affiliations

  1. Division of Cardiology, Montreal Children’s Hospital, 2300 Tupper Street, H3H 1P3, Montreal, Quebec, Canada

    Andrew S. Mackie

  2. Department of Cardiology, Children’s Hospital Boston, Boston, MA, 02115, USA

    Andrew S. Mackie, Peter Lang & Andrew J. Powell

  3. Department of Pediatrics, Harvard Medical School, Boston, MA, 02115, USA

    Andrew S. Mackie, Peter Lang & Andrew J. Powell

Authors
  1. Andrew S. Mackie
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  2. Peter Lang
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  3. Andrew J. Powell
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Correspondence to Andrew S. Mackie.

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Mackie, A.S., Lang, P. & Powell, A.J. Pulmonary Atresia with Intact Ventricular Septum Coexisting with Coarctation of the Aorta. Pediatr Cardiol 28, 406–408 (2007). https://doi.org/10.1007/s00246-006-1411-3

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  • DOI: https://doi.org/10.1007/s00246-006-1411-3

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