Pediatric Cardiology

, Volume 27, Issue 5, pp 621–623 | Cite as

Coarctation of the Aorta in the Right Aortic Arch with Left Aberrant Innominate Artery

  • Shelli BeinEmail author
  • Ziad Saba
  • Hitendra Patel
  • Olaf Reinhartz
  • Frank L. Hanley


Right aortic arch with an aberrant left innominate artery is a rare combination. We report a unique case of coarctation of the aorta in a patient with right aortic arch and aberrant left innominate artery. The diverticulum of Kommerell gave rise to the left innominate artery and a left ligamentum arteriosum, completing a vascular ring. This unusual case raises interesting points regarding the development of coarctation in the context of a right-sided arch and the approach to management of these patients.


Coarctation Right aortic arch Left aberrant innominate artery Diverticulum of Kommerell 


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Copyright information

© Springer Science+Business Media, Inc. 2006

Authors and Affiliations

  • Shelli Bein
    • 1
    • 2
    Email author
  • Ziad Saba
    • 1
  • Hitendra Patel
    • 1
  • Olaf Reinhartz
    • 1
  • Frank L. Hanley
    • 1
  1. 1.Departments of Cardiology and Cardiothoracic SurgeryChildren’s Hospital and Research Center at OaklandOaklandUSA
  2. 2.Columbia University Medical CenterMedical School for International HealthNew YorkUSA

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