Pediatric Cardiology

, Volume 27, Issue 5, pp 604–607 | Cite as

A Criss-Cross Heart with Twisted Atrioventricular Connections, “Perfect Streaming,” and Double Discordance

  • Walter J. DuncanEmail author
  • Kenny K. Wong
  • Robert M. Freedom


At 24 weeks gestational age, a term female infant was diagnosed with complex congenital heart disease. The antenatal cardiac diagnosis was uncertain and included univentricular heart. Following delivery, the child remained well and was normally saturated. Echocardiography and angiocardiography revealed an unusual relationship between atria and ventricles.


Criss-cross heart Atrioventricular and ventriculoarterial discordance 



We thank Dr. James Potts for his assistance with the manuscript.


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Copyright information

© Springer Science+Business Media, Inc. 2006

Authors and Affiliations

  • Walter J. Duncan
    • 1
    Email author
  • Kenny K. Wong
    • 1
  • Robert M. Freedom
    • 2
  1. 1.Department of Pediatrics, Division of CardiologyUniversity of British Columbia, British Columbia Children’s HospitalVancouverCanada
  2. 2.Department of Pediatrics, Division of CardiologyUniversity of Toranto, The Hospital for Sick ChildrenTorontoCanada

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