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Persistent Atrial Standstill in Noncompaction Cardiomyopathy

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Atrial standstill is a rare form of bradyarrhythmia and consists of a transitory or permanent loss of the electrical and mechanical activity of the atria. It has been described in a few cases of long-standing valvular disease, amyloidosis, myocarditis, and muscular dystrophy. We report on a young female with noncompaction cardiomyopathy that progressed to congestive heart failure. Electrocardiogram showed persistence atrial standstill that was confirmed clinically and by electrocardiomyopathy, Doppler two-dimensional echocardiogram, and tissue Doppler imaging. We assume that worsening of asymptomatic noncompaction and progression to the congestive form of cardiomyopathy could be presaged by the presence of persistent atrial standstill. Thus, persistence of atrail standstill in asymptomatic cardiomyopathy is a sign of poor prognosis.

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  1. Amat-y-Leon F, Racki AJ, Denes P, et al. (1974) Familial atrial dysrhythmia with A-V block: intracellular microelectrode, clinical electrophysiologicm, and morphologic observations. Circulation 50:1097–1104

    PubMed  CAS  Google Scholar 

  2. Bensaid J (1996) Persistent atrial standstill documented over a 22-year period. Am Heart J 131:404–407

    Article  PubMed  CAS  Google Scholar 

  3. Chin TK, Perloff JK, Williams RG, Jue K, Mohrman R (1990) Isolated noncompaction of left ventricular myocardium; a study of eight cases. Circulation 82:507–513

    PubMed  CAS  Google Scholar 

  4. Ichida F, Hanamichi Y, Miyawaki T, et al. (1999) Clinical features of isolated A.-A A. noncompaction of the ventricular myocardium: long-term clinical course, hemodynamic properties, and genetic background. J Am Coll Cardiol 34:233–240

    Article  PubMed  CAS  Google Scholar 

  5. Jeong MH, ahn YK, Gill GC, et al. (1996) Tsutsugamushi myocarditis with congestive heart failure and persistent atrial standstill. Jpn Circ J 60:382–388

    Article  PubMed  CAS  Google Scholar 

  6. Marini M, Arbustini E, Disertori M (2004) Atrial standstill: a paralysis of cardiological relevance. Ital Heart J Suppl 5:681–686

    PubMed  Google Scholar 

  7. Oechslin EN, Jost CHA, Rojas JR, Kaufinann PA, Jenni R (2000) Long-term follow-up of 34 adults with isolated left ventricular noncompaction; a distinct cardiomyopathy with poor prognosis. J Am Coll Cardiol 36:493–500

    Article  PubMed  CAS  Google Scholar 

  8. Rigopoulos A, Rizos IK, Aggeli C, et al. (2002) Isolated left ventricular noncompaction: an unclassified cardiomyopathy with severe prognosis in adults. Cardiology 98:25–32

    Article  PubMed  Google Scholar 

  9. Ritter M, Oechslin E, Sutsch G, et al. (1997) Isolated noncompaction of the myocardium in adults, Mayo Clinic Proc 72:26–31

    Article  CAS  Google Scholar 

  10. Shah MK, Subramanvan R, Tharakan J, Venkitachalam KG (1992) Familial total atrial standstill. Am Heart J 123:1379–1382

    Article  PubMed  CAS  Google Scholar 

  11. Talwar KK, Radhakrishnan S, Chopra P (1988) Myocarditis manifesting as persistent atrial standstill. Int J Cardiol 20:283–286

    Article  PubMed  CAS  Google Scholar 

  12. Ward DE, Ho SY, Shinebourne EA (1984) Familial atrial standstill and inexcitability in childliood. Am J Cardiol 53:965–967

    Article  PubMed  CAS  Google Scholar 

  13. Williams DO, Joness EL, Nagle B, Smith S (1972) Familial atrial cardiomyopathy with heart block. Q J Med 41:491–508

    PubMed  CAS  Google Scholar 

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Correspondence to A.A. El Menyar.

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Menyar, A.E., Gendi, S. Persistent Atrial Standstill in Noncompaction Cardiomyopathy. Pediatr Cardiol 27, 364–366 (2006).

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