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Successful One-Stage Repair of Unilateral Agenesis of Pulmonary Artery

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Abstract

Unilateral agenesis of the pulmonary artery is a rare congenital anomaly that is commonly associated with ventricular septal defect (VSD). Its clinical presentation is diverse, and if left untreated, it can lead to significant damage and even death. Several surgical techniques have been developed for its management, with variable results. We report the case of a 2-month-old infant with agenesis of the left pulmonary artery (PA) and VSD. One-stage primary surgical re-anastomosis was successful in establishing continuity to the main PA and preventing further damage to the heart.

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Statement of Ethics

This case report was written in compliance with the regulations of the Human Research and Ethics Committee of King Fahad National Guard Hospital, Riyadh, Saudi Arabia, Data regarding the patient’s clinical status were collected by chart review, Patient confidentiality was maintained throughout data collection and manuscript preparation.

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Authors and Affiliations

  1. Section of Pediatric Cardiology, King Abdulaziz Cardiac Center, King Fahad National Guard Hospital, P.O. Box 22490, Riyadh, 11426, Saudi Arabia

    M.A. Hamdan & Y. Al Meshham

  2. Section of Cardiovascular Surgery, King Abdulaziz Cardiac Center, King Fahad National Guard Hospital, P.O. Box 22490, Riyadh, 11426, Saudi Arabia

    H.K. Najm

Authors
  1. M.A. Hamdan
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  2. Y. Al Meshham
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  3. H.K. Najm
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Correspondence to M.A. Hamdan.

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Hamdan, M., Meshham, Y.A. & Najm, H. Successful One-Stage Repair of Unilateral Agenesis of Pulmonary Artery. Pediatr Cardiol 26, 724–726 (2005). https://doi.org/10.1007/s00246-005-0927-2

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  • DOI: https://doi.org/10.1007/s00246-005-0927-2

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