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Circumoral complications in hereditary sensory and autonomic neuropathy — a case of simple lip reconstruction?

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Abstract

We report a case of a 7-year-old Bangladeshi boy who caused himself oral incontinence by self-mutilation. The patient was known to suffer from hereditary sensory and autonomic neuropathy type V. As definitive management, a full dental clearance was performed along with reconstruction of the lower lip with a good functional and aesthetic outcome. He did not experience any adverse effects from the full dental clearance with regard to feeding, nutrition or development. We discuss the dilemma and challenges raised in the management of this patient and highlight the need for a multi-disciplinary specialist input for what appeared to be a simple case of lip reconstruction for a plastic surgeon.

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Authors and Affiliations

  1. Department of Plastic Surgery, Royal Manchester Children’s Hospital, Oxford Road, Manchester, M13 9WL, UK

    Tomas Madura & Mamta Shah

  2. Department of Surgical and Perioperative Science, Section of Hand and Plastic Surgery, Umeå University, Umeå, Sweden

    Alex McGrath

  3. Dental Health Unit, Royal Manchester Children’s Hospital, Oxford Road, Manchester, M13 9WL, UK

    Kay Hood

Authors
  1. Tomas Madura
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  2. Alex McGrath
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  3. Kay Hood
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  4. Mamta Shah
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Correspondence to Mamta Shah.

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Madura, T., McGrath, A., Hood, K. et al. Circumoral complications in hereditary sensory and autonomic neuropathy — a case of simple lip reconstruction?. Eur J Plast Surg 36, 319–321 (2013). https://doi.org/10.1007/s00238-012-0704-4

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  • DOI: https://doi.org/10.1007/s00238-012-0704-4

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