Idiopathic hypertrophic pachymeningitis: spectrum of the disease

Abstract

Hypertrophic pachymeningitis is extremely rare. It is a fibrosing inflammatory process which involves the dura mater, including the tentorium. Numerous pathological entities produce thickening of the pachymeninges, so that idopathic hypertrophic pachymeningitis is a diagnosis of exclusion. We describe four patients with idiopathic hypertrophic pachymeningitis who had varied clinical presentation. Imaging studies revealed diffuse thickening of the pachymeninges; in one patient there was extensive dural sinus thrombosis. Since no identifiable cause was found, the cases were labelled as idiopathic.

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Received: 4 July 1996 Accepted: 1 November 1996

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Goyal, M., Malik, A., Mishra, N. et al. Idiopathic hypertrophic pachymeningitis: spectrum of the disease. Neuroradiology 39, 619–623 (1997). https://doi.org/10.1007/s002340050479

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  • Key words Idiopathic hypertrophic pachymeningitis
  • Magnetic resonance imaging