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Schizencephaly with occlusion or absence of middle cerebral artery

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Abstract

In a study of 160 infants with prenatal and/or perinatal risk factors for brain damage, we observed three cases of schizencephaly. All cases were unilateral, and the clefts had open lips. In two cases, magnetic resonance angiography showed occlusion or absence of the middle cerebral artery (MCA) on the affected side. Two of the patients, including one with absent flow in the MCA of the affected side, had ipsilateral cerebellar atrophy.

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Acknowledgements

This project was partially supported by grants 36263M of CONACyT and SALUD-2002 C01-7074 of CONACyT. The authors acknowledge technical assistance of engineer Hector Belmont Tamayo, M. in Sc.; Juan José Ortiz Retana; and Ms. Pilar Galarza. They also acknowledge Dr. Dorothy Pless for revising the English version of the manuscript.

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Correspondence to A. Fernández-Bouzas.

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Fernández-Bouzas, A., Harmony, T., Santiago-Rodríguez, E. et al. Schizencephaly with occlusion or absence of middle cerebral artery. Neuroradiology 48, 171–175 (2006). https://doi.org/10.1007/s00234-005-0006-7

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  • DOI: https://doi.org/10.1007/s00234-005-0006-7

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