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Vaginal vault prolapse in a patient with Mayer–Rokitansky–Küster–Hauser syndrome: a video case presentation

Abstract

Introduction and hypothesis

Several reports have described vaginal prolapse in Mayer–Rokitansky–Küster–Hauser (MRKH) syndrome patients after creation of a neovagina. To our knowledge, no reports of primary vaginal prolapse of a blind pouch without previous intervention, or surgery for this condition, have been described.

Methods

In this case report, we describe a 19-year-old woman with MRKH and complete prolapse of her shortened vaginal pouch. Surgical correction utilizing permanent suture-based sacrospinous ligament fixation was performed.

Results

The patient had a successful outcome.

Conclusions

Sacrospinous ligament fixation provided a safe and effective method for the management of vaginal pouch prolapse. Long-term follow-up is planned. To our knowledge, this is the first report describing surgical repair of primary prolapse of a blind vaginal pouch in the setting of MRKH.

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Correspondence to Carolyn Botros.

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A rare case of a young woman with vaginal prolapse (MP4 55059 kb)

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Botros, C., Iyer, S., Tran, A.M. et al. Vaginal vault prolapse in a patient with Mayer–Rokitansky–Küster–Hauser syndrome: a video case presentation. Int Urogynecol J 28, 1747–1749 (2017). https://doi.org/10.1007/s00192-017-3325-4

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  • DOI: https://doi.org/10.1007/s00192-017-3325-4

Keywords

  • Mayer–Rokitansky–Küster–Hauser syndrome
  • Vaginal vault prolapse