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Der Gynäkologe

, Volume 50, Issue 11, pp 867–878 | Cite as

Pubertätsstörungen beim Mädchen

Wie früh ist zu früh und wie spät zu spät?
  • Esther M. Nitsche
CME
  • 165 Downloads

Zusammenfassung

Pubertas praecox und Pubertas tarda sind im Wesentlichen anhand statistisch ermittelter Kriterien definiert. Diese Definitionen beschreiben zunächst nur den Pubertätsbeginn in Relation zur Gesamtbevölkerung und implizieren noch keine Pathologie. Neben Normvarianten können einer Pubertätstempostörung verschiedene, ganz unterschiedliche Erkrankungen zugrunde liegen. Die Ursachen reichen von „idiopathischen“ Störungen über Tumoren, endokrinologische, immunologische und genetische Erkrankungen bis hin zu psychosomatischen und psychiatrischen Krankheitsbildern. Im Beitrag sollen die Abgrenzung einer möglichen Pathologie gegen die sehr viel häufigere Normvariante erläutert und die Differenzialdiagnosen der wichtigsten abklärungsbedürftigen und therapiepflichtigen Krankheitsbilder dargestellt werden.

Schlüsselwörter

Pubertas praecox  Säkularer Trend Pubertas tarda Hypogonadismus Ullrich-Turner-Syndrom 

Disorders of puberty in young girls

How early is too early and how late is too late?

Abstract

Precocious and delayed puberty are statistical definitions, which are initially based on anthropological data in relation to the total population and mathematical calculations. They do not automatically imply a pathology. Besides normal variations a large number of very different underlying disorders can result in alteration of the onset and/or course of pubertal development. These range from idiopathic disturbances, endocrinological and immunological diseases, genetic variations and tumors up to psychosomatic and psychiatric diseases. In this article, the emphasis is on the differential diagnostics between the very much more common and non-pathological normal variations and the most important diseases that need further clarification and subsequent treatment.

Keywords

Precocious puberty Secular trend Delayed puberty Hypogonadism Ullrich–Turner syndrome 

Notes

Einhaltung ethischer Richtlinien

Interessenkonflikt

E.M. Nitsche gibt an, dass kein Interessenkonflikt besteht.

Dieser Beitrag beinhaltet keine von den Autoren durchgeführten Studien an Menschen oder Tieren.

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Copyright information

© Springer Medizin Verlag GmbH 2017

Authors and Affiliations

  1. 1.Praxis für Kinder- und Jugendmedizin Dr. med. Esther Maria NitscheLübeckDeutschland

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