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Ebstein-Anomalie des Fetus

Ebstein’s anomaly of the fetus

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Der Gynäkologe Aims and scope

Zusammenfassung

Die bereits in der Fetal- und/oder Neonatalzeit symptomatische Form der Ebstein-Anomalie ist ein schweres Krankheitsbild mit hoher intrauteriner und neonataler Mortalität. Intrauterin können kardiale Insuffizienzen und Hydrops auftreten, postpartal gelingt es oft nicht, eine ausreichende Lungenperfusion und Herzauswurf zu sichern. Neue Aspekte der intrauterinen Überwachung, des perinatalen und postnatalen Managements werden ausführlich diskutiert.

Abstract

The form of Ebstein’s anomaly that is already symptomatic in utero is a severe disease that is associated with a high intrauterine as well as neonatal mortality. Cardiac insufficiency and hydrops may already occur in utero; in the postnatal period establishment of sufficient pulmonary perfusion and/or cardiac output often fails. This review focuses on new aspects of intrauterine monitoring, as well as peri- and postnatal management in these patients.

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Authors and Affiliations

  1. Abteilung für Geburtshilfe und Pränatale Medizin, Universitätsklinikum Bonn,

    U. Gembruch, T. Kohl, A. Geipel & C. Berg

  2. Abteilung für Kinderkardiologie, Universitätsklinikum Bonn,

    U. Herberg & J. Breuer

  3. Abteilung für Geburtshilfe und Pränatale Medizin, Zentrum für Geburtshilfe und Frauenheilkunde am Universitätsklinikum Bonn, Sigmund-Freud-Straße 25, 53105, Bonn,

    U. Gembruch

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  1. U. Gembruch
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  2. T. Kohl
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  3. A. Geipel
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  4. U. Herberg
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  5. J. Breuer
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Correspondence to U. Gembruch.

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Gembruch, U., Kohl, T., Geipel, A. et al. Ebstein-Anomalie des Fetus. Gynäkologe 39, 39–47 (2006). https://doi.org/10.1007/s00129-005-1785-y

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