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Retroperitoneales Leiomyosarkom

Eine seltene Differentialdiagnose des Nebennierentumors

Retroperitoneal leiomyosarcoma

A rare differential diagnosis of an adrenal tumor

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Zusammenfassung

Eine pararenale Raumforderung ist ein Befund, der auch gegenwärtig präoperativ nicht immer hinsichtlich des Ursprungsorgans abgeklärt werden kann. Wir berichten im Folgenden von einem Patienten, der mit seit mehreren Monaten bestehenden dumpfen Flanken- und Oberbauchschmerzen aufgenommen worden war. Die Ultraschalluntersuchung bei Aufnahme zeigte einen großen soliden homogenen Tumor im Bereich des oberen linken Nierenpols. Bei unauffälligem Urinstatus und unauffälligen Katecholaminen in Serum und Harn fand sich intraoperativ ein die Nierenkapsel und die V. renalis infiltrierendes Leiomyosarkom. Auch bei Anwendung moderner bildgebender Verfahren muss bei im Bereich der Nebenniere gelegenen Raumforderungen insbesondere bei negativen Laborbefunden auch ein extraadrenaler Tumor erwogen werden.

Abstract

A pararenal mass is a clinical finding that cannot be explored preoperatively regarding its parent organ even nowadays. We report in the following about a patient who was admitted with dull pain located in the flank and upper abdomen. Ultrasound investigation at admission showed a solid homogeneous mass close to the upper pole of the left kidney. Urinalysis and catecholamine levels were normal. Intraoperatively, a sarcoma infiltrating the renal capsule and renal vein was observed. In the case of a mass located in the area of the adrenal gland, an extra-adrenal tumor must be considered especially if there are normal findings for urinalysis and catecholamine levels even if modern imaging techniques had been applied.

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Authors and Affiliations

  1. Urologische Klinik, Marien-Hospital, Marl

    J. Hodzic

  2. Institut für Arbeitsphysiologie, Universität, Dortmund

    K. Golka

  3. Abteilung Urologie, Chirurgische Universitätsklinik, Ruprecht-Karls Universität, Heidelberg

    K. Möhring & G. Riedasch

  4. Urologische Klinik, Marien-Hospital, Hervester Straße 57, 45768, Marl

    J. Hodzic

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  1. J. Hodzic
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  2. K. Golka
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  3. K. Möhring
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  4. G. Riedasch
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Correspondence to J. Hodzic.

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Hodzic, J., Golka, K., Möhring, K. et al. Retroperitoneales Leiomyosarkom. Urologe 45, 209–214 (2006). https://doi.org/10.1007/s00120-005-0930-5

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  • DOI: https://doi.org/10.1007/s00120-005-0930-5

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