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Bilaterale spontane Karotisdissektion bei Osteogenesis imperfecta (Typ I)

Bilateral spontaneous carotid artery dissection in osteogenesis imperfecta (type I)

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Zusammenfassung

Wir berichten über einen 36-jährigen Patienten mit linkshirnigem Mediainfarkt infolge beidseitiger spontaner A.-carotis-interna-Dissektionen bei Osteogenesis imperfecta (OI) Typ I. Spontane Dissektionen hirnversorgender Arterien stellen eine der häufigsten Hirninfarktursachen bei jüngeren Patienten dar. Unser Fall belegt, dass bei „spontanen“ Hirnarteriendissektionen immer nach einer angeborenen Bindegewebsschwäche gefahndet werden sollte. Die Identifizierung einer bislang nicht bekannten angeborenen Bindegewebsschwäche kann wesentlich zur Primär- und Sekundärprophylaxe des Hirninfarktes beitragen.

Summary

We report on a 36-year-old patient with an acute cerebral infarction due to a spontaneous dissection of both internal carotid arteries in conjunction with type I osteogenesis imperfecta. Spontaneous dissections of cerebral arteries (DCA) represent a common cause of cerebral infarctions in younger patients. Our case shows that a hereditary connective tissue disorder should be considered in all patients with „spontaneous“ DCA. The identification of an – initially unknown – hereditary connective tissue disorder may contribute to primary and secondary prophylaxis of cerebral ischemia.

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Authors and Affiliations

  1. Neurologische Klinik, Universitätsklinikum des Saarlandes, Kirrberger Straße, 66421, Homburg/Saar, Deutschland

    C. Becker, K. Fassbender &  J. Spiegel

  2. Klinik für Diagnostische und Interventionelle Neuroradiologie, Universitätsklinikum des Saarlandes, Homburg/Saar, Deutschland

    C. Roth & W. Reith

Authors
  1. C. Becker
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  2. C. Roth
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  3. W. Reith
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  4. K. Fassbender
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  5. J. Spiegel
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Correspondence to J. Spiegel.

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Becker, C., Roth, C., Reith, W. et al. Bilaterale spontane Karotisdissektion bei Osteogenesis imperfecta (Typ I). Nervenarzt 80, 1222–1225 (2009). https://doi.org/10.1007/s00115-009-2860-8

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