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Neurokutane Angiomatose

Manifestation mit zystischen Raumforderungen

Neurocutaneous angiomatosis

Manifestation with cystic tumors

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Zusammenfassung

Eine 54-jährige Patientin entwickelte eine Gangstörung und epileptische Anfälle. Das CCT zeigte multiple zystische intrazerebrale Raumforderungen. Histologisch konnten diese als Blutungshohlräume mit angiomatösen Malformationen im Randbereich identifiziert werden. Im Beobachtungszeitraum von 7 Jahren zeigen diese Phasen spontaner Regression und Progression. Gleichzeitig fanden sich multiple kutane Hämangiome. Die Erkrankung ist als ungewöhnliche Form einer neurokutanen Angiomatose anzusehen.

Summary

A 54-year-old woman developed epilepsy and gait disorder. The initial CCT showed multiple intracerebral cysts. Histologically these turned out to be cavities from repetitive bleedings out of abnormal vessels in the border region. Regular observation during 7 years showed spontaneous episodes of regression and progression of the cysts. In addition, multiple hemangiomas of the skin were found. The case presented here represents an unusual manifestation of neurocutaneous angiomatosis.

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Authors and Affiliations

  1. Neurologische Klinik, Krankenhaus Barmherzige Brüder, Regensburg

    C. Isenberg & H. L. Kolmann

  2. Neurologische Klinik, Krankenhaus Barmherzige Brüder, Prüfeningerstraße 86, 93049, Regensburg

    C. Isenberg

Authors
  1. C. Isenberg
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  2. H. L. Kolmann
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Correspondence to C. Isenberg.

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Isenberg, C., Kolmann, H.L. Neurokutane Angiomatose. Nervenarzt 76, 202–204 (2005). https://doi.org/10.1007/s00115-004-1780-x

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  • DOI: https://doi.org/10.1007/s00115-004-1780-x

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