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Partielle Aplasie des Atlasbogens beim Kind

Partial aplasia of the atlas in a child

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Zusammenfassung

Kongenitale Fehlbildungen des Atlasbogens sind relativ selten und können in unterschiedlichen Formen auftreten. Diese reichen von partiellen Unterbrechungen des hinteren oder des vorderen Bogens bis hin zur vollständigen Agenesie. Häufig werden diese Anomalien erst erkannt, wenn es aufgrund eines Traumas zu einer radiologischen Untersuchung der Halswirbelsäule kommt. Die Abgrenzung dieser kongenitalen Varianten von Frakturen des Atlas ist wichtig, um unnötige diagnostische, aber auch (neuro-)chirurgische Interventionen zu vermeiden. Im Folgenden wird der Fall eines 10 Jahre alten Mädchens beschrieben, das nach einem Sturz aus geringer Höhe in der Notaufnahme vorgestellt wurde und radiologisch eine Aplasie des hinteren Atlasbogens aufwies. Diagnostische und therapeutische Vorgehensweisen werden diskutiert.

Abstract

Congenital anomalies of the atlas are rare but well documented. They can range from total agenesis to partial clefts of the posterior and/or anterior arches and are mostly incidental findings after a sustained trauma. It is essential to differentiate these congenital variants from fractures of the atlas to prevent the patient from unnecessary (neuro-) surgical intervention. In this article the case of a 10-year-old girl is described with an unusual finding of partial aplasia of the posterior arch. The clinical features and diagnostic and therapeutic procedures are discussed.

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Correspondence to C.A. Kühne.

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Bliemel, C., Kuehl, H., Ruchholtz, S. et al. Partielle Aplasie des Atlasbogens beim Kind. Unfallchirurg 112, 513–516 (2009). https://doi.org/10.1007/s00113-008-1534-5

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