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Ein Fallbericht zur Hüftendoprothesenimplantation bei Osteopetrosis ossificans

Pseudarthrose des Oberschenkelhalses

Case report: total hip replacement for osteopetrosis ossificans

Femoral neck nonunion

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Zusammenfassung

Wir berichten über einen Patienten, bei dem die operative Versorgung einer schmerzhaften Pseudarthrose des Schenkelhalses durch die Marmorknochenkrankheit (Osteopetrosis ossificans) erschwert wurde. Die Operationsplanung und die technische Vorgehensweise der Implantation einer sonderangefertigten Hüfttotalendoprothese sowie das frühzeitige postoperative Ergebnis wird vorgestellt. Die in der Literatur vorgestellten Fälle mit Oberschenkelhalsfraktur, Pseudarthrose des Oberschenkelhalses und totalem Hüftgelenkersatz bei Osteopetrosis werden diskutiert.

Abstract

This is a report about a young patient with marble bone disease who suffered from femoral neck nonunion after operative treatment of a dislocated femoral neck fracture. We discuss the treatment options, explain the technical procedure and the difficulties involved in preparations for total hip replacement with a custom-made femoral stem, and present the early postoperative result. Furthermore we comment on cases reported in the literature of patients with marble bone disease and femoral neck fracture, femoral neck nonunion, and total hip replacement.

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  1. Berufsgenossenschaftliche Unfallklinik, Friedberger Landstraße 430, 60389, Frankfurt/M., Deutschland

    O. Schoierer & R. Hoffmann

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  1. O. Schoierer
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  2. R. Hoffmann
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Correspondence to O. Schoierer.

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Schoierer, O., Hoffmann, R. Ein Fallbericht zur Hüftendoprothesenimplantation bei Osteopetrosis ossificans. Unfallchirurg 110, 784–788 (2007). https://doi.org/10.1007/s00113-007-1266-y

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