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Seltene Weichgewebstumoren an seltener Lokalisation

Glomustumoren bei einem 16-jährigen Jungen

Rare presentation of soft tissue tumors in uncommon locations

Glomus tumors in a 16-year-old boy

  • Kasuistiken
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Zusammenfassung

Kasuistik

Bei einem 16-jährigen Jungen wurden 3 bläuliche, teils schmerzhafte, subkutane Raumforderungen reseziert. Die Histologie ergab multiple, disseminierte Glomustumoren.

Charakteristika von Glomustumoren

Es handelt sich um seltene benigne Weichgewebstumoren, ausgehen von den Glomuskörperchen, welche die Thermoregulation v. a. an den Akren steuern. Glomustumoren treten meist solitär bei Frauen im Erwachsenenalter auf, nur in 10 % der Fälle wird ein multiples Vorkommen beobachtet, dann v. a. bei männlichen Jugendlichen.

Behandlung von Glomustumoren

Die Therapie der Wahl ist die Exzision. Die Rezidivrate beträgt 12–50 %.

Abstract

Case report

Three bluish, partly painful, subcutaneous lesions in a 16-year-old boy were resected. The histology showed multiple, disseminated glomus tumors.

Characteristics of glomus tumors

Glomus tumors are rare benign soft tissue tumors, arising from the glomus apparatus. Glomus bodies predominantly control thermoregulation in the extremities. In most cases, glomus tumors occur as solitary tumors in adult women. Multiple glomus tumors only occur in 10 % of cases, particularly in male adolescents.

Therapy of glomus tumors

Radical resection is the treatment of choice. The recurrence rate ranges from 12 to 50 %.

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Einhaltung ethischer Richtlinien

Interessenkonflikt. A. Burger, B. Klein, S. Weih, P. Günther und S. Holland-Cunz geben an, dass kein Interessenkonflikt besteht. Dieser Beitrag beinhaltet keine Studien an Menschen oder Tieren.

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Authors and Affiliations

  1. Kinderchirurgie, Chirurgische Klinik, Universitätsklinikum Heidelberg, Im Neuenheimer Feld 110, 69120, Heidelberg, Deutschland

    A. Burger, B. Klein, P. Günther & S. Holland-Cunz

  2. Chirurgische Universitätsklinik, Universitätsklinikum Freiburg, Freiburg, Deutschland

    S. Weih

Authors
  1. A. Burger
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  2. B. Klein
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  3. S. Weih
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  4. P. Günther
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  5. S. Holland-Cunz
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Correspondence to A. Burger.

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Burger, A., Klein, B., Weih, S. et al. Seltene Weichgewebstumoren an seltener Lokalisation. Monatsschr Kinderheilkd 162, 150–152 (2014). https://doi.org/10.1007/s00112-013-3029-x

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