Zusammenfassung
Gastrointestinale Atresien sind wesentlicher Bestandteil kinderchirurgischer Krankheitsbilder. Sie können in unterschiedlicher Häufigkeit die Speiseröhre, den Magenausgang, Darmabschnitte oder das Anorektum betreffen und gehen häufig mit anderen Fehlbildungen einher. Die Ätiologie der Atresien ist nicht einheitlich und kann auf gestörte Entwicklungsprozesse, genetische Abweichungen oder Durchblutungsstörungen zurückgeführt werden. Gemeinsam ist den Atresien die Notwendigkeit der interdisziplinären Versorgung an spezialisierten Zentren durch Kinderchirurgen, Pädiater und Vertreter anderer Fachbereiche, die Erfahrung mit diesen seltenen Fehlbildungen haben. Dies gilt nicht nur für die Therapie, sondern auch für die Nachbetreuung, die für die meisten Atresieformen bis ins Erwachsenenalter erforderlich ist.
Abstract
Gastrointestinal atresias represent an important group of congenital malformations in the field of pediatric surgery. They may affect all intestinal segments from the esophagus to the anorectum and are often accompanied by anomalies of other organs. The etiology of the different atresias is not uniform and is characterized by disrupted developmental processes, genetic abnormalities or impaired blood supply of the affected organ. All atresias share the need for interdisciplinary care and therapy in specialized centers by pediatric surgeons, pediatricians and representatives of other medical subspecialities experienced in the treatment of these rare anomalies. This is not only important for initial therapy but also for follow-up which is essential for most atresias until adulthood.
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Dingemann, C., Ure, B. Gastrointestinale Atresien. Monatsschr Kinderheilkd 159, 1213–1220 (2011). https://doi.org/10.1007/s00112-011-2493-4
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DOI: https://doi.org/10.1007/s00112-011-2493-4
Schlüsselwörter
- Gastrointestinale Atresien
- Kongenitale Fehlbildungen
- Prä- und postnatale Diagnostik
- Interdisziplinäre Therapie
- Prognose und Nachsorge