Zusammenfassung
Seit Mitte der 1980er Jahre ist es möglich, Patienten, die an einem hypoplastischen Linksherzsyndrom leiden, einer operativen Versorgung zuzuführen. Im ersten Schritt derselben werden der hypoplastische Aortenbogen rekonstruiert und die Durchblutung der Lunge mittels Shunt sichergestellt. In weiteren Schritten werden System- und Pulmonalkreislauf wieder getrennt – mit passiver Durchblutung der Lunge und Optimierung der Arbeit des rechten Systemventrikels. Dieses operative Prozedere stellt einen Standard dar, der den Patienten hilft, mit guter Lebensqualität zu überleben.
Abstract
Since the middle of the 1980s it has been possible to palliate patients suffering from hypoplastic left heart syndrome. In the first step the hypoplastic aortic arch is reconstructed and the lung is perfused by a shunt. In the further surgical step a separation of systemic and pulmonary circulation is performed. The pulmonary perfusion remains passive and the work load of the right ventricle will be optimized. This operative procedure has now become a standard procedure and helps these patients to survive with a good quality of life.
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Weinzettel, R., Mair, R., Tulzer, G. et al. Hypoplastisches Linksherzsyndrom . Monatsschr Kinderheilkd 158, 930–937 (2010). https://doi.org/10.1007/s00112-010-2175-7
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DOI: https://doi.org/10.1007/s00112-010-2175-7