Zusammenfassung
Der vorliegende Bericht beschreibt den Fall einer 77-jährigen Patientin mit einem Leiomyosarkom der subhepatischen V. cava inferior. Symptomatisch bestanden unspezifische Oberbauchschmerzen. In der Sonographie und Computertomographie wurde ein primärer Lebertumor vermutet, in der Magnetresonanztomographie wurde die retroperitoneale Lokalisation der Raumforderung erkannt. Der Tumor konnte komplett reseziert werden, die V. cava inferior wurde durch eine Gefäßprothese ersetzt. Vaskuläre Leiomyosarkome sind sehr seltene Tumoren, sie werden häufig erst im fortgeschrittenen Stadium entdeckt und können je nach Lokalisation mit anderen Tumoren verwechselt werden.
Abstract
This case report describes a 77-year old woman with a leiomyosarcoma of subhepatic inferior caval vein. The presented symptom was unspecific abdominal pain. Ultrasound and CT suggested a primary liver tumor. MRI revealed retroperitoneal location of the neoplasm. The tumor was resected completely and ICV was replaced by a PTF-graft. Vascular leiomyosarcoma is a rare tumor entity, which often is diagnosed in advanced stage. Depending on location it can be mistaken for neoplasms of other organs.
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Kinkel, B., Walgenbach-Brünagel, G., Risse, J. et al. Seltene Differenzialdiagnose bei Verdacht auf Lebertumor. Internist 50, 612–616 (2009). https://doi.org/10.1007/s00108-008-2278-6
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DOI: https://doi.org/10.1007/s00108-008-2278-6