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Anetodermisches Pilomatrikom

Seltene Variante eines häufigen Adnextumors im Kindesalter

Anetodermic pilomatricoma

Uncommon variant of a common childhood adnexal tumor

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Zusammenfassung

Der anetodermische („bullöse“) Typ ist eine seltene Variante des Pilomatrikoms, die wir bei 2 Mädchen im Alter von 9 und 10 Jahren diagnostizierten. Klinisch imponierten die Tumoren als 3 × 2 bzw. 1,5 × 1,5 cm große, rötliche, halbkugelige Vorwölbungen mit leicht gefälteter Oberfläche am oberen Rücken bzw. prätibial. Oberflächlich tasteten sie sich auffallend weich, in der Tiefe hart. Histologisch zeigte sich über einem tief gelegenen, typischen Pilomatrikom ein ödematöses, gefäßreiches Korium, das an Granulationsgewebe erinnerte. Klinische und histologische Besonderheiten des anetodermischen Pilomatrikoms werden anhand der bisher publizierten Fälle besprochen.

Abstract

The anetodermic (“bullous”) subtype is a rare variant of pilomatricoma which we diagnosed in 2 girls who were 9 and 10 years old. The tumors presented as 3 × 2 and 1.5 × 1.5 cm red dome-shaped nodules with a slightly wrinkled surface on the upper back and on the pretibial region, respectively. Both were superficially soft, but then firm as one palpated deeper. Histology showed an edematous, well-vascularized dermis resembling granulation tissue overlying a deep otherwise typical pilomatricoma. Clinical and histological characteristics of the anetodermic subtype are discussed on the basis of previously published cases.

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Einhaltung ethischer Richtlinien

Interessenkonflikt. F. Karademir, A. Kerstan und H. Hamm geben an, dass kein Interessenkonflikt besteht. Dieser Beitrag beinhaltet keine Studien an Menschen oder Tieren.

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Authors and Affiliations

  1. Klinik und Poliklinik für Dermatologie, Venerologie und Allergologie, Universitätsklinikum Würzburg, Josef-Schneider-Str. 2, 97080, Würzburg, Deutschland

    F. Karademir, A. Kerstan & H. Hamm

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  1. F. Karademir
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  2. A. Kerstan
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  3. H. Hamm
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Correspondence to F. Karademir.

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Karademir, F., Kerstan, A. & Hamm, H. Anetodermisches Pilomatrikom. Hautarzt 65, 59–62 (2014). https://doi.org/10.1007/s00105-013-2663-5

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  • DOI: https://doi.org/10.1007/s00105-013-2663-5

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