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Kutaner maligner peripherer Nervenscheidentumor bei Neurofibromatose Typ 1

Cutaneous malignant peripheral nerve sheath tumor in neurofibromatosis type 1

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Zusammenfassung

Patienten mit Neurofibromatose haben ein gegenüber der Normalbevölkerung erhöhtes Risiko, Malignome zu entwickeln. Wir berichten über eine Patientin, bei der sich ein maligner peripherer Nervenscheidentumor aus einem präexistenten Neurofibrom entwickelte.

Abstract

Patients with neurofibromatosis have an increased risk of developing malignant tumors in comparison to the general population. We describe a woman who developed a malignant peripheral nerve sheath tumor in a pre-existing neurofibroma.

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Authors and Affiliations

  1. Klinik für Dermatologie, Allergologie und Umweltmedizin, St. Barbara-Hospital, Katholisches Klinikum Duisburg, Barbarastraße 67, 47167, Duisburg, Deutschland

    V. Dietrich, J. Schaller & J. Kunze

  2. Dermatohistologisches Labor, Duisburg, Deutschland

    J. Schaller

Authors
  1. V. Dietrich
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  2. J. Schaller
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  3. J. Kunze
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Correspondence to V. Dietrich.

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Dietrich, V., Schaller, J. & Kunze, J. Kutaner maligner peripherer Nervenscheidentumor bei Neurofibromatose Typ 1. Hautarzt 60, 830–833 (2009). https://doi.org/10.1007/s00105-008-1700-2

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  • DOI: https://doi.org/10.1007/s00105-008-1700-2

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