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Coexistence of congenital heart anomalies with noncompaction of the ventricular myocardium

Two case reports

Angeborene Herzfehler bei gleichzeitigem Vorliegen einer ventrikulären Noncompaction-Kardiomyopathie

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  • Case study
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Abstract

Noncompaction of the ventricular myocardium (NVM) is a rare cardiac anomaly which can lead to the development of cardiomyopathy. NVM can be isolated or associated with congenital heart anomalies such as ventricular septal defect, atrial septal defect, pulmonic stenosis, bicuspid aortic valve, and Ebstein anomaly. NVM usually presents with heart failure symptoms, ventricular tachyarrhythmias, and thromboembolic events. We report two cases of NVM, one associated with a ventricular septal defect and other associated with bicuspid aortic valve.

Zusammenfassung

Die fehlende Verdichtung des ventrikulären Myokards [“noncompaction of the ventricular myocardium“ (NVM)] ist ein seltener Herzfehler, aus dem sich eine Kardiomyopathie entwickeln kann. Eine NVM kann isoliert vorliegen oder mit angeborenen Herzfehlern assoziiert sein, so beispielsweise mit einem Ventrikelseptum- oder Vorhofseptumdefekt, einer Pulmonalstenose, einer bikuspidalen Aortenklappe und einer Ebstein-Anomalie. Die NVM äußert sich gewöhnlich durch Symptome einer Herzinsuffizienz, ventrikuläre Tachyarrhythmien und thromboembolische Ereignisse. Wir berichten über 2 Patienten mit NVM, im einen Fall assoziiert mit einem Ventrikelseptumdefekt, im anderen mit einer bikuspidalen Aortenklappe.

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The corresponding author states that there are no conflicts of interest.

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Authors and Affiliations

  1. Osmaniye State Hospital, Cardiology Clinic, 80000, Osmaniye, Turkey

    A. Doğan MD & H. Aksoy

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  1. A. Doğan MD
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  2. H. Aksoy
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Correspondence to H. Aksoy.

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Doğan, A., Aksoy, H. Coexistence of congenital heart anomalies with noncompaction of the ventricular myocardium. Herz 37, 699–701 (2012). https://doi.org/10.1007/s00059-012-3582-4

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  • DOI: https://doi.org/10.1007/s00059-012-3582-4

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