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Spontane Skleraperforation bei zirkumskripter Sklerodermie (en coup de sabre)

Spontaneous scleraperforation in a case of linear scleroderma (en coup de sabre)

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Zusammenfassung

Bei einem 55jährigen Patienten mit Sklerodermie „en coup de sabre“ kam es zu spontaner Filterkissenbildung, anhaltender Bulbushypotonie und ausgeprägter Aderhautfaltenbildung, die den Fistelverschluß durch lamelläre Keratoplastik notwendig machten. Befunde und Verlauf während der vierjährigen Nachbeobachtung werden beschrieben.

Summary

A 55-year-old patient with known scleroderma “en coup de sabre” presented with a spontaneous covered scleraperforation. The persisting bulbus hypotony and prominent choroidal folds made a lamellar keratoplasty necessary. Findings and course within the four year follow up period are discussed.

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Literatur

  1. Aberer E, Neumann R, Stanek G (1985) Is localized scleroderma a borrelia infection? Lancet 2: 278

    Article  PubMed  CAS  Google Scholar 

  2. Ashton N, Coomes EN, Garner A, Oliver DO (1968) Retinopathy due to progressive systemic sclerosis. J Pathol 96: 259–261

    Article  CAS  Google Scholar 

  3. Behrendt S, Eckardt C (1990) Postoperative nekrotisierende Sklerokeratitis. Klin Monatsbl Augenheilkd 197: 503–505

    Article  PubMed  CAS  Google Scholar 

  4. Cormane RH, Hamerlinck F, Nunzi E (1979) Antibodies eluted from lymphoid cell membrane. Arch Dermatol 115: 709

    Article  PubMed  CAS  Google Scholar 

  5. Duke-Elder St (1968) System of ophthalmology Bd 8/2, London

  6. Farkas TG, Sylvester V, Archer D (1972) The choroidopathy of progressive systemic sclerosis (scleroderma). Am J Ophthalmol 74: 875–886

    PubMed  CAS  Google Scholar 

  7. Foster CS (1987) Ocular manifestations of the nonrheumatic acquired collagen vascular diseases. In: Smolin G, Thoft RA (eds) The Cornea: Scientific foundations and clinical practice. Little, Brown and Comp, p 361–363

  8. Gerke E, Meyer-Schwickerath G, Joussen F (1976) Sklerodermie en coup de sabre mit spontaner Filterkissenbildung. Klin Monatsbl Augenheilkd 168: 426–428

    PubMed  CAS  Google Scholar 

  9. Gold DH (1989) Ocular manifestations of connective tissue (collagen) diseases. In: Tasman W, Jaeger EA (eds) Duane’s clinical ophthalmology. Lippincott, Philadelphia 5/26: 21–23

    Google Scholar 

  10. Horan EC (1969) Ophthalmic manifestations of progressive systemic sclerosis. Br J Ophthalmol 53: 388–392

    Article  PubMed  CAS  Google Scholar 

  11. Kirkham TH (1969) Scleroderma and Sjögren’s syndrome. Br J Ophthalmol 53: 131–133

    Article  PubMed  CAS  Google Scholar 

  12. Lindenmuth KA, Sugar A, Kincaid MC, Nelson CC, Comstock CP (1988) Invasive squamous cell carcinoma of the conjunctiva presenting as necrotizing scleritis with scleral perforation and uveal prolapse. Surv Ophthalmol 33: 50–54

    Article  PubMed  CAS  Google Scholar 

  13. Manschot WA (1965) Generalized scleroderma with ocular symptoms. Ophthalmologica 149: 131–137

    PubMed  CAS  Google Scholar 

  14. MacLean H, Guthrie W (1969) Retinopathy in scleroderma. Trans Ophthalmol Soc UK 89: 209

    Google Scholar 

  15. Mensing H (1990) Zirkumskripte Sklerodermie. Dtsch Dermatologe 8: 944–946

    Google Scholar 

  16. Steuhl KP, Richard G, Weidle EG (1985) Clinical observations concerning choroidal folds. Ophthalmologica 190: 219–224

    Article  PubMed  CAS  Google Scholar 

  17. Stucchi CA, Geiser JD (1967) Manifestations oculaires de la sclerodermie generalisée (Points communs avec le syndrome de Sjögren). Doc Ophthalmol 22: 72

    Article  PubMed  CAS  Google Scholar 

  18. Suttorp-Schulten MSA, Koorneef L (1990) Linear scleroderma associated with ptosis and motility disorders. Br J Ophthalmol 74: 694–695

    Article  PubMed  CAS  Google Scholar 

  19. Tan EM, Rodnan GP (1975) Profile of antinuclear antibodies in progressive systemic sclerosis (PSS) (abstract). Arthritis Rheum 18: 430

    Google Scholar 

  20. Tang RA, Mewis-Christmann L, Wolf J, Wilkens RB (1986) Pseudooculomotor palsy presenting sign of linear scleroderma. J Pediatr Ophthalmol Stabismus 23: 236–238

    CAS  Google Scholar 

  21. Taylor P, Talbot EM (1985) Perilimbal vascular anomaly associated with ipsilateral en coup de sabre morphoea. Br J Ophthalmol 69: 60–62

    Article  PubMed  CAS  Google Scholar 

  22. West RH, Barnett AJ (1979) Ocular involvement in scleroderma. Br J Ophthalmol 63: 845–847

    Article  PubMed  CAS  Google Scholar 

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Authors and Affiliations

  1. Universitäts-Augenklinik Tübingen Abt. I: Allgemeine Augenheilkunde mit Poliklinik, Deutschland

    W. Bachmann & H. J. Thiel

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  1. W. Bachmann
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  2. H. J. Thiel
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Bachmann, W., Thiel, H.J. Spontane Skleraperforation bei zirkumskripter Sklerodermie (en coup de sabre). Spektrum Augenheilkd 5, 213–216 (1991). https://doi.org/10.1007/BF03163861

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  • DOI: https://doi.org/10.1007/BF03163861

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