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Neuropsychologische kenmerken van kinderen en adolescenten met een (lichte) verstandelijke beperking

Profielen in relatie tot etiologie

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Kind en adolescent

Abstract

Ramakers, G. J. A., & Ponsioen, A. J. G. B. (2007). Neuropsychological characteristics of children and adolescents with (mild) mental retardation. Profiles in relation to etiology, Kind en Adolescent, 28 (3), 119-134.

Neuropsychological assessment has demonstrated that different syndromic forms of intellectual disability, in addition to a global deficiency in cognitive functioning, can be characterized by a specific pattern of stronger and weaker abilities. In this article we describe findings obtained in neuropsychological studies of children and adolescents with borderline and mild mental retardation, and of several syndromic forms of mental retardation. Knowledge of the cognitive profile of individuals with intellectual disability can be used to generate more directed, evidence-based support which should promote the functioning and wellbeing of the person involved. From a developmental perspective, significant gains could be attained, in particular with children and adolescents with borderline and mild mental retardation.

Keywords: mild mental retardation, syndromes, neuropsychology.

Samenvatting

Neuropsychologisch onderzoek naar verschillende syndromale vormen van een verstandelijke beperking (vb) heeft laten zien dat er naast een globale deficiëntie in het cognitief functioneren sprake kan zijn van een specifiek patroon van relatief sterkere en zwakkere cognitieve vaardigheden. In dit artikel zullen bevindingen worden beschreven uit neuropsychologisch onderzoek bij jongeren met een licht verstandelijke beperking (lvb) en een aantal syndromale vormen van vb. Inzicht in het cognitieve profiel van individuen met een vb kan worden aangewend om tot een meer gerichte, evidence-based ondersteuning te komen, waardoor het functioneren en het welzijn bevorderd zouden kunnen worden. Vanuit het ontwikkelingsperspectief van kinderen en adolescenten met een lvb zou hierdoor belangrijke winst kunnen worden geboekt.

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Authors and Affiliations

  1. www.bsl.nl/shop/kind-en-adolescent-0167-2436.html

    Ger J. A. Ramakers

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  1. Ger J. A. Ramakers
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  2. Albert J. G. B. Ponsioen
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Correspondence to Ger J. A. Ramakers.

Additional information

Dr. G. J. A. Ramakers, neurobioloog en klinisch ontwikkelingspsycholoog, is werkzaam bij de Programmagroep Ontwikkelingspsychologie van de Universiteit van Amsterdam en het Nederlands Instituut voor Neurowetenschappen te Amsterdam.

Contactadres: dr. G. J. A. Ramakers, Neuronen en Netwerken, Nederlands Instituut voor Neurowetenschappen, Meibergdreef 47, 1105 BA Amsterdam zo, e-mail: G.Ramakers@nin.knaw.nl

Dr. A. J. G. B. Ponsioen, gz-psycholoog, is werkzaam bij ggz Dijk en Duin Driehuis, team Cognitieve Beperkingen.

Weblinks

http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?CMD=search&DB=omim

omim: Online Mendelian Inheritance in Man: onderdeel van PubMed met uitgebreide informatie over genetische syndromen

http://www.ssbp.co.uk/ssbp/pages/about-ssbp.php

Society for the Study of Behavioural Phenotypes: informatie over gedragseigenschappen van diverse cognitieve ontwikkelingssyndromen.

http://www.nih.knaw.nl/~ramakers /

De website van dr. Ramakers met informatie over onderzoek naar verstandelijke handicap

http://www.fvo.nl /

Federatie van Ouderverenigingen; overkoepelende organisatie van diverse verenigingen van ouders met verstandelijk gehandicapte kinderen, met links naar specifieke syndromen.

http://www.erfelijkheid.nl /

Website van het Erfocentrum, het Nationale Kennis- en Voorlichtingscentrum Erfelijkheid

http://www.lvgnet.nl /

Landelijk Kenniscentrum lvg, met onderzoeksinformatie over personen met lichte verstandelijke beperkingen

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Ramakers, G.J.A., Ponsioen, A.J.G.B. Neuropsychologische kenmerken van kinderen en adolescenten met een (lichte) verstandelijke beperking. KIAD 28, 78–87 (2007). https://doi.org/10.1007/BF03061025

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