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Congenital cholesteatoma of the middle ear and petrous bone

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An Erratum to this article was published on 01 October 1995

Abstract

A retrospective analysis of 51 cases of congenital cholesteatoma of the middle ear and the petrous bone is reported. Of the 44 congenital middle ear cholesteatomas, 21 were localised to the posterosuperior mesotympanum and this was in complete contrast to the commonly reported anterosuperior location which was seen in only 2 cases. The remaining 21 patients had cholesteatoma involving mesotympanum and/or epitympanum. All the patients except one were treated using a closed tympanoplasty. A second stage procedure was performed in 33 patients. Residual disease was seen in 19 (57%) patients undergoing second stage surgery. Thirtyeight (85%) patients had a preoperative air bone gap of 30 dB or more. Of the 33 patients considered for hearing results, 16 (48%) had a postoperative gap within 10 dB.

Amongst the 7 congenital petrous bone cholesteatomas, facial nerve dysfunction and sensorineural deafness were the commonest symptoms. The modified transcochlear approach was the most preferred approach in management of these patients.

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Authors and Affiliations

  1. Gruppo Otologico, Via Emmanueli 42, 29100, Piaccnza, Italy

    Sandeep Karmarkar

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  1. Sandeep Karmarkar
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An erratum to this article is available at http://dx.doi.org/10.1007/BF03047991.

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Karmarkar, S. Congenital cholesteatoma of the middle ear and petrous bone. IJO & HNS 47, 95–100 (1995). https://doi.org/10.1007/BF03047935

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