Zusammenfassung
Es wird eine Patientin mit akuten Kopfschmerzen, leichten kognitiven Störungen ohne fokales neurologisches Defizit vorgestellt. Das MRT zeigt multiple kleine Hirninfarkte; angiographisch wurden segmentale Lumeneinengungen zerebraler Gefäße gefunden. Die vollständige Remission unter alleiniger Corticoidtherapie, angiographisch und in mehreren MRT dokumentiert, unterstützt die Diagnose eines benignen Typs der primären Angiitis des Zentralnervensystems.
Summary
A female patient with sudden onset of headache, mild decreased cognition without focal neurologic deficit is reported. MRI showed multiple bilateral supratentorial infarcts; cerebral angiography demonstrated segmental narrowing of cerebral vessels. The complete clinical remission under treatment with corticosteroids, angiographically and MRI confirmed, sustained the diagnosis of a benign subset of the primary angiitis of central nervous system.
Literatur
Abu Shakra M, Khraishi M, Grosman H et al. Primary angiitis of the CNS diagnosed by angiography. J Med 1994; 87:351–8.
Alhalabi M, Moore PM. Serial angiography in isolated angiitis of the central nervous system. Neurology 1994;44:1221–6.
Calabrese LH. Vasoulitis of the central nervous system. Rheum Dis Clin North Am 1995;21:1059–68.
Calabrese LH, Gragg LA, Furlan AJ. Benign angiopathy: a distinct subset of angiographically defined primary angiitis of the central nervous system. J Rheumatol 1993;20:2046–50.
Calabrese LH, Mallek JA. Primary angiitis of the central nervous system: report of eight new cases, review of the literature and proposal for diagnostic criteria. Medicine 1988;67:20–39.
Cravioto H, Feigin I. Noninfectious granulomatous angiitis with a predilection for the nervous system. Neurology, 1959;9: 599–609.
Ehsan T, Hasan S, Powers JM et al. Serial magnetic resonance imaging of isolated angiitis of the central nervous system. Neurology 1995;45:1462–5.
Lie JT. Primary (granulomatous) angiitis of the central nervous system: a clinicopathological analysis of 15 new cases and a review of the literature. Hum Pathol 1992;23:164–71.
Ozawa T, Sasaki O, Sorimachi T et al. Primary angiitis of the central nervous system: report of two cases and review of the literature. Neurosurgery 1995;36:173–9.
Vollmer TL, Guarnaccia J, Harrington W et al. Idiopathic granulomatous angiitis of the central nervous system. Arch Neurol 1993;50:925–30.
Author information
Authors and Affiliations
Rights and permissions
About this article
Cite this article
Popescu-Pretor, R., Turk, J. Primäre Angiitis des Zentralnervensystems: Gibt es einen benignen Subtyp?. Klin Neuroradiol 8, 42–46 (1998). https://doi.org/10.1007/BF03044067
Received:
Accepted:
Issue Date:
DOI: https://doi.org/10.1007/BF03044067