Abstract
Arthrogryposis Multiplex Congenita (AMC) describes a rare multifactorial syndrome caused by a variety of neurogenic and myopathic disorders first diagnosed at birth and often progressing to a state of significant disability. It includes abnormalities of the cardiovascular, respiratory, nervous and genitourinary systems. The syndrome is seen primarily in the paediatric population, and orthopedic procedures are common. There remains much confusion regarding diagnosis, aetiology, genetic probabilities, natural history and management.1-2 Occasionally an adult with this sydrome presents for an anaesthetic.
The following is a case report of a patient with the manifestations of this syndrome presenting for a primary Caesarean section.
Résumé
La conduite anesthêsique chez une femme âgée de 21 ans atteinte ďarthrogrypose congénitale et devant subir une césarienne élective est décrite. Ľanesthésie régionale fut tentée mais sans succès. Ľanesthésie générale ainsi qu’une discussion des différentes considérations est présentée. La conduite anesthêsique dépend surtout sur des manifestations spécifiques individuelles et les problèmes associés.
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Quance, D.R. Anaesthetic management of an obstetrical patient with arthrogryposis multiplex congenita. Can J Anaesth 35, 612–614 (1988). https://doi.org/10.1007/BF03020349
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DOI: https://doi.org/10.1007/BF03020349