Conclusion
In this review, principles for the management of anaesthesia for children with congenital syndromes have been outlined, with little reference to specific drugs or techniques. Thus, newer drugs or approaches, which may not yet appear in case reports or in the older literature on the syndromes, may be considered appropriate according to the clinical experience of the anaesthetist who has an understanding of the problems created by the presence of an individual syndrome. Genetics is relevant in the emerging emphasis on the role of anaesthetists as perioperative physicians. However, the future is in the drug response variability and pain response aspects.
Conclusion
Dans cette mise à jour, les principes de conduite anesthésique pour les enfants porteurs de syndromes congénitaux ont été énoncés, avec peu d’emphase sur les médicaments et techniques spécifiques. Ainsi, les nouveaux médicaments ou les nouvelles approches, qui n’apparaissent pas encore dans les présentations de cas ou dans la littérature plus ancienne concernant les syndromes, pourront être considérés appropriés selon l’expérience clinique de l’anesthésiste, bien au fait des problèmes créés par chacun des syndromes. La génétique est très appropriée à la nouvelle vocation de l’anesthésiste comme médecin de la période périopératoire. Cependant, le futur réside dans la variabilité des réponses médicamenteuses ainsi que des réponses à la douleur.
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Bevan, J.C. Congenital syndromes in paediatric anaesthesia: what is important to know. Can J Anaesth 45 (Suppl 1), R3–R16 (1998). https://doi.org/10.1007/BF03019203
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DOI: https://doi.org/10.1007/BF03019203