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Wildervanck’s syndrome

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Abstract

The association of congenital cervical synostosis typical of the Klippel-Feil deformity with eye-ball retraction, abducens nerve palsy, and hearing loss first described by Wildervanck in 1952 is reviewed. Conductive, as well as sensorineural hearing losses have since been described. Polytomography, in our case, demonstrates a unilateral bulbous vestibule and dilated semicircular canal with basilar impression of the skull. A Duane’s retraction syndrome of the eyes was discovered.

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Authors and Affiliations

  1. Greater Baltimore Medical Center, 6701 North Charles Street, 21204, Baltimore, Maryland, USA

    Gopesh K. Sharma

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  1. Gopesh K. Sharma
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Sharma, G.K. Wildervanck’s syndrome. Indian J Otolaryngol 31, 108–110 (1979). https://doi.org/10.1007/BF02992408

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  • DOI: https://doi.org/10.1007/BF02992408

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