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An epidemiological study on children with syndromic hearing loss

Indian Journal of Otolaryngology and Head and Neck Surgery volume 56, pages 208–212 (2004)Cite this article

Abstract

Objectives: To study the epidemiological factors in children with syndromic hearing loss.

Study design: Interview based prospective study.

Settings: Govt. ENT Hospital, AYJNIHH, NIMH-SEC, and Schools for the Deaf-in Hyderabad and Secunderabad

Patients: Children aged below 14 years, with hearing loss, their parents/guardians.

Intervention(s): The study revealed type and degree of hearing impairment. In high risk groups genetic counseling was offered.

Results: Epidemiological studies were carried out in 743 children below 14 years with hearing impairment and 138 (18.57%) were found to have syndromic deafness. Majority of the children with hearing loss have an association of ocular abnormality (22.46%, n=31) followed by skeletal anomalies 14.49% (n=20) and dental anomalies (10.86%). We observed 24 cases (3.21%) with genetically well recognized syndromes.

Conclusion: Data is generated on epidemiological and etiology of Hearing Impairment. Hearing Impairment is due to both environmental and genetic causes. Environmental factors in 17 (13.77%), genetically inherited 21 cases (15.22%) and the cause is not known in the remaining cases. Such a data is required in order to offer genetic counseling to reduce the genetic burden.

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Affiliations

  1. Department of ENT, Osmania Medical College, Begumpet Hyderabad - 500 016, Andhra Pradesh

    M. V. V. Reddy, V. V. V. Sathyanarayana & P. P. Reddy

  2. Institute of Genetics and Hospital for Genetic Diseases, Osmania University, Begumpet Hyderabad - 500 016, Andhra Pradesh

    V. Sailakshmi, L. Hemabindu & P. Usha Ran

Authors
  1. M. V. V. Reddy
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  2. V. V. V. Sathyanarayana
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  3. V. Sailakshmi
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  4. L. Hemabindu
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  5. P. Usha Ran
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  6. P. P. Reddy
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Reddy, M.V.V., Sathyanarayana, V.V.V., Sailakshmi, V. et al. An epidemiological study on children with syndromic hearing loss. Indian J Otolaryngol Head Neck Surg 56, 208–212 (2004). https://doi.org/10.1007/BF02974352

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  • DOI: https://doi.org/10.1007/BF02974352

Key Words

  • Epidemiology
  • Syndrome
  • Consanguinity