Résumé
Les tumeurs stromales gastrointestinales (GIST) sont les tumeurs mésenchymateuses les plus fréquentes du tractus gastro-intestinal. Elles sont positives pour le c-kit (CD117). Elles sont plus fréquentes chez l’homme adulte et se localisent la plupart du temps dans l’estomac et moins fréquemment dans le côlon, le rectum et l’œsophage. La GIST rectale survient peu fréquemment et la GIST anale est encore plus rare. La résection chirurgicale est le traitement de choix pour les GIST résécables ainsi que pour les autres tumeurs mésenchymateuses bénignes ou malignes. Elles seront le plus souvent traitées par une amputation abdomino-périnéale.
Un diagnostic de nature et un staging précis préopératoire sont indispensables pour une prise en charge optimale. Nous rapportons ici le cas d’une patiente porteuse d’une GIST du canal anal et discuterons des caractéristiques de cette entité peu fréquente.
Summary
Gastrointestinal stromal tumors (GISTs) are the most common mesenchymal tumors of the gastrointestinal tract. They are positive to c-kit (CD117), more frequent in adult male, and are mostly found in the stomach, more rarely in the colon, rectum and oesophagus. Rectal GIST is uncommon, and anal GIST is even rarer. Surgery is the treatment of choice for resectable GISTs, and for other benign or malignant mesenchymal tumours. Surgery treatment consist of abdomino-perineal resection. Preoperative pathological diagnosis and staging are required. We hereafter report the case of one patient with anal GIST and discuss the characteristics of this rare entity.
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Gillard, P., Marques, C.C., Meunier, P. et al. GIST anale. Acta Endosc 37, 63–75 (2007). https://doi.org/10.1007/BF02961817
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DOI: https://doi.org/10.1007/BF02961817