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Vasodilator therapy of pulmonary hypertension in the crst syndrome

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Summary

TWO patients with the CRST syndrome and pulmonary hypertension are described. They were treated with hydralazine given orally in a dosage of 200 mgs daily. One patient improved subjectively and had a better exercise capacity but the signs of pulmonary hypertension and tricuspid regurgitation persisted. The other patient has shown a marked clinical improvement and a significant reduction of the pulmonary hypertension has been demonstrated on repeat cardiac catheterisation.

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McWeeney, J., Finnegan, P. Vasodilator therapy of pulmonary hypertension in the crst syndrome. Ir J Med Sci 151, 151–154 (1982). https://doi.org/10.1007/BF02940166

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