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Intravenous alpha-1-antitrypsin replacement therapy: Case report after one year of treatment

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Abstract

Alpha-1-antitrypsin deficiency is an autosomaliy inherited disease in which individuals homozygous for the disorder are prone to develop severe emphysema. We report the case of a 43 yr old man with severe deficiency and advanced emphysema and the first experience in Ireland with intravenous alpha-l-antitrypsin replacement. After I yr of replacement therapy we report our experience with dosage and frequency of infusion as well as pulmonary function test data before and during treatment.

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Authors and Affiliations

  1. Mater Misericordiae Hospital, Eccles Street, 7, Dublin

    A. C. Ward & B. A. Keogh

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  1. A. C. Ward
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  2. B. A. Keogh
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Ward, A.C., Keogh, B.A. Intravenous alpha-1-antitrypsin replacement therapy: Case report after one year of treatment. I.J.M.S. 166, 7–9 (1997). https://doi.org/10.1007/BF02939766

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