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Basic aspects of cystic fibrosis

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References

  1. Quinton, P. M., Martinez, J. R, and Hopfer, U. (eds.) (1982),Fluid and Electrolyte Abnormalities in Exocrine Glands in Cystic Fibrosis, San Francisco Press, San Francisco.

    Google Scholar 

  2. DeVault, J. D., Berry, A., Misra, T. K., Darzins, A., and Chakrabarty, A. M. (1989),Biotech 7, 352–357.

    Article  CAS  Google Scholar 

  3. Taylor, C. J., Baxter, P. S., Hardcastle, J., and Hardcastle, P. T. (1988),Gut 29, 957–962.

    Article  PubMed  CAS  Google Scholar 

  4. Berschneider, H. M., Knowles, M. R, Azizkhan, R. G., Boucher, R, Tobey, N. A., Orlando, R. C., and Powell, D. W. (1988),FASEB J. 2, 2625–2629.

    PubMed  CAS  Google Scholar 

  5. Bijman, J., Kansen, M., Hoogeveen, A. H., Scholte, B., van der Kamp, A., and de Jonge, H. (1988),Exocrine Secretion (Wong, P. Y. D. and Young, J. A., eds.), Hong Kong University Press, Hong Kong, pp. 17–19.

    Google Scholar 

  6. Kopelman, H., Forstner, G., Durie, P., and Corey, M. (1989),Clin. Invest. Med. 12, 207–211.

    PubMed  CAS  Google Scholar 

  7. Durie, P. R. and Forstner, G. G. (1989),J. R. Soc. Med. 82, 2–10.

    PubMed  Google Scholar 

  8. Kopelman, H., Corey, M., Gaskin, K., Durie, P., Weizman, Z., and Forstner, G. (1988),Gastroenterology 95, 349–355.

    PubMed  CAS  Google Scholar 

  9. Brugman, S. M. and Taussig, L. M. (1984),Cystic Fibrosis (Taussig, L. M., ed.), Thieme-Stratton Inc., New York, pp. 323–337.

    Google Scholar 

  10. Kopito, L. E., Kosasky, H. J., and Shwachman, H. (1973),Fertil. Steril. 24, 512–516.

    PubMed  CAS  Google Scholar 

  11. di Sant’ Agnese, P. A., Darling, R. C., Perera, G. A., and Shea, E. (1953),Amer. J. Med. 15, 777–184.

    Article  CAS  Google Scholar 

  12. Shwachman, H. and Mahmoodian, A. (1967),Mod. Prob. Pediatr. 10, 158–182.

    Google Scholar 

  13. di Sant’ Agnese, P. A. and Hubbard, V. S. (1984)Cystic Fibrosis (Taussig, L. M., ed.), Thieme-Stratton Inc., New York, pp. 296–322.

    Google Scholar 

  14. Lloyd-Still, J. D. (ed.) (1984),Textbook of Cystic Fibrosis. PSG, John Wright, Boston, MA.

    Google Scholar 

  15. Taussig, L. M. (ed.) (1984),Cystic Fibrosis. Thieme-Stratton Inc., New York.

    Google Scholar 

  16. Mastella, G. and Quinton, P. (eds.) (1988),Cellular and Molecular Basis of Cystic Fibrosis. San Francisco Press, Berkeley.

    Google Scholar 

  17. Riordan, J. R. and Buchwald, M. (eds.) (1986),Genetics and Epithelial Cell Dysfunction in CF. Alan Liss, New York.

    Google Scholar 

  18. Quinton, P. M. (1983),Nature (London),301, 421–422.

    Article  CAS  Google Scholar 

  19. Bijman, J. and Quinton, P. M. (1984),Am. J. Physiol. 247, C3-C9.

    PubMed  CAS  Google Scholar 

  20. Knowles, M. R., Stutts, M. J., Spock, A., Fischer, N., Gatzy, J. T., and Boucher, R. C. (1983),Sci. 221, 1067–1069.

    Article  CAS  Google Scholar 

  21. Quinton, P. M. (1986),Am. J. Physiol. 251, C649-C652.

    PubMed  CAS  Google Scholar 

  22. Bijman, J. and Frömter, E. (1986),Pflüg Arch. 407, S123-S127.

    Article  CAS  Google Scholar 

  23. Sato, K. and Sato, F. (1984),J. Clin. Invest. 73, 1763–1771.

    Article  PubMed  CAS  Google Scholar 

  24. Rommens, J. M., Iannuzzi, M. C., Kerem, B.-S., Drumm, M. L., Melmer, G., Dean, M., Rozmahel, R., Cole, J. L., Kennedy, D., Hidaka, N., Zsiga, M., Buchwald, M., Riordan, J. R., Tsui, L.-C., and Collins, F. S. (1989),Sci. 245, 1059–1065.

    Article  CAS  Google Scholar 

  25. Riordan, J. R., Rommens, J. M., Kerem, B.-S., Alon, N., Rozmahel, R., Grzelczak, Z., Zielenski, J., Lok, S., Plavsic, N., Chou, J.-L., Drumm, M. L., Iannuzzi, M. C., Collins, F. S., and Tsui, L.-C. (1989),Sci. 245, 1066–1073.

    Article  CAS  Google Scholar 

  26. Kerem, B.-S., Rommens, J. M., Buchanan, J. A., Markiewicz, D., Cox, T. K., Chakravarti, A., Buchwald, M., and Tsui, L.-C. (1989),Sci. 245, 1073–1080.

    Article  CAS  Google Scholar 

  27. Wright, S. W. and Morton, N. E. (1968),Am. J. Hum. Gen. 20, 157–169.

    CAS  Google Scholar 

  28. Quinton, P. M. (1982),Fluid and Electrolyte Abnormalities in Exocrine Glands in Cystic Fibrosis (Quinton, P. M., Martinez, J. R., and Hopfer, U., eds.), San Francisco Press, San Francisco, pp. 53–76.

    Google Scholar 

  29. Wine, J. J. (1988),Cellular and Molecular Basis of Cystic Fibrosis (Mastella, G. and Quinton, P. M., eds.), San Francisco Press, San Francisco, pp 33–46.

    Google Scholar 

  30. Bradley, G., Juranka, P. F., and Ling, V. (1988),Biochem. Biophys. Acta 948, 87–128.

    PubMed  CAS  Google Scholar 

  31. Thiebaut, F., Tsuruo, T., Hamada, H., Gottesman, M. M., Pastan, I., and Willingham, M. C. (1987),Proc. Natl. Acad. Sci. USA 84, 7735–7738.

    Article  PubMed  CAS  Google Scholar 

  32. Mimmack, M. L., Gallagher, M. P., Pearce, S. R., Hyde, S. C., Booth, I. R., and Higgins, C. F. (1989),Proc. Natl. Acad. Sci. USA 86, 8257–8261.

    Article  PubMed  CAS  Google Scholar 

  33. Gumbiner, B. (1987),Am. J. Physiol. 253, C749-C758.

    PubMed  CAS  Google Scholar 

  34. Almers, W. and Sterling, C. (1984),J. Membr. Biol. 77, 169–186.

    Article  PubMed  CAS  Google Scholar 

  35. Frizzell, R. A., Field, M., and Schultz, S. G. (1979),Am. J. Physiol. 236, 1–8.

    Google Scholar 

  36. Welsh, M. J. (1987),Physiol Rev. 67, 1143–1184.

    PubMed  CAS  Google Scholar 

  37. Powell, D. W. (1986),Physiology of Membrane Disorders, 2nd Ed. (Andreoli, T. E., Hoffman, J. F., Fannestil, D. D., and Schultz, S. G., eds.), Plenum Press, New York, pp. 559–583.

    Google Scholar 

  38. Reddy, M. M. and Quinton, P. M. (1989),Am. J. Physiol. C727-C735.

  39. Willumsen, N. J. and Boucher, R. C. (1989),Am. J. Physiol. 256, C1054-C1063.

    PubMed  CAS  Google Scholar 

  40. Ling, B. N. and Eaton, D. C. (1989),Am. J. Physiol. 256, F1094-F1103.

    PubMed  CAS  Google Scholar 

  41. Widdicombe, J. H., Welsh, M. J., and Finkbeiner, W. E. (1985),Proc. Natl. Acad. Sci. USA 82, 6167–6171.

    Article  PubMed  CAS  Google Scholar 

  42. Boucher, R. C., Cotton, C. U., Gatzy, J. T., Knowles, M. R., and Yankaskas, J. R. (1988),J. Physiol. 405, 77–103.

    PubMed  CAS  Google Scholar 

  43. Cullen, J. J. and Welsh, M. J. (1987),J. Clin. Invest. 79, 1–7.

    Article  Google Scholar 

  44. Durand, J. and Lehmann, C. (1989),Comp. Biochem. Physiol. 94A, 173–178.

    Article  CAS  Google Scholar 

  45. Sato, K., Kang, W. H., Saga, K., and Sato, K. T. (1989),J. Am. Acad. Derm. 20, 537–563.

    PubMed  CAS  Google Scholar 

  46. Quinton, P. M. (1987),Kidney Intl. 32, 102–108.

    Article  Google Scholar 

  47. Behm, J. K., Hagiwara, G., Lewiston, N. J., Quinton, P. M., and Wine, J. J. (1986),Pediatr. Res. 22, 271–276.

    Article  Google Scholar 

  48. Peterson, J. W. and Ochoa, L. G. (1989),Sci. 245, 857–859.

    Article  CAS  Google Scholar 

  49. Widdicombe, J. H. (1986),Am. J. Physiol. 251, R818-R822.

    PubMed  CAS  Google Scholar 

  50. Welsh, M. J. (1986),Pflüg. Arch. 407, S116-S122.

    Article  CAS  Google Scholar 

  51. Welsh, M. J. and Liedtke, C. M. (1986),Nature 322, 467–470.

    Article  PubMed  CAS  Google Scholar 

  52. Frizzell, R. A., Rechkemmer, G., and Shoemaker, R. L. (1986),Sci. 233, 558–560.

    Article  CAS  Google Scholar 

  53. Schoumacher, R. A., Shoemaker, R. L., Halm, D. R., Tallant, E. A., Wallace, R. W., and Frizzell, R. A. (1987),Nature 330, 752–754.

    Article  PubMed  CAS  Google Scholar 

  54. Li, M., McCann, J. D., Liedtke, C. M., Nairn, A. C., Greengard, P., and Welsh, M. J. (1988),Nature 331, 358–360.

    Article  PubMed  CAS  Google Scholar 

  55. Hwang, T.-C., Lu, L., Zeitlin, P. L., Gruenert, D. C., Huganir, R., and Guggino, W. B. (1989),Sci. 244, 1351–1356.

    Article  CAS  Google Scholar 

  56. Jetten, A. M., Yankaskas, J. R., Stutts, M. J., Williamson, N. J., and Boucher, R. C. (1989),Sci. 244, 1472–1475.

    Article  CAS  Google Scholar 

  57. Chen, J. H., Schulman, H., and Gardner, P. (1989),Sci. 243, 657–660.

    Article  CAS  Google Scholar 

  58. Hamill, O. P., Marty, A., Neher, E., Sakmann, B., and Sigworth, F. J. (1981),Pflüg. Arch. 391, 85–100.

    Article  CAS  Google Scholar 

  59. Sakmann, B. and Neher, E. (1983),Single-Channel Recording (Sakmann, B. and Neher, B. eds.), Plenum Press, New York, pp. 37–51.

    Google Scholar 

  60. Krouse, M. E., Hagiwara, G., Chen, J. H., Lewiston, N. J., and Wine, J. J. (1989),Am. J. Physiol. 257, C129-C140.

    PubMed  CAS  Google Scholar 

  61. Joris, L., Krouse, M. E., Hagiwara, G., Bell, C. L., and Wine, J. J. (1989),Pflüg. Arch. 414, 369–372.

    Article  CAS  Google Scholar 

  62. Hagiwara, G., Krouse, M. E., Müller, U. J., and Wine, J. J. (1989),Sci. 246, 1049–1050.

    Article  CAS  Google Scholar 

  63. Hagiwara, G., Krouse, M. E., Müller, U. J., Ward, C. L., Law, T. C., and Wine, J. J. (1989),Ped. Pulmon. suppl. 4, 124.

  64. Müller, U. J., Krouse, M. E., Hagiwara, G., Ward, C. L., Law, T. C., and Wine, J. J. (1989),Ped. Pulmon. suppl. 4, 125.

  65. Krouse, M. E., Hagiwara, G., Müller, U. J., Ward, C. L., Law, T. C., and Wine, J. J. (1989),Ped. Pulmon. suppl. 4, 117.

  66. Lew, T. S., Wood, L., and Krasne, S. (1989),Ped. Pulmon. suppl. 4, 117.

  67. Li, M., McCann, J. D., Anderson, M. P., Clancy, J. P., Liedtke, C. M., Nairn, A. C., Greengard, P., and Welsh, M. J. (1989),Sci. 244, 1353–1356.

    Article  CAS  Google Scholar 

  68. Bear, C. E. (1988),FEBS Lett. 237, 145–149.

    Article  PubMed  CAS  Google Scholar 

  69. Willumsen, N. J. and Boucher, R. C. (1989),Am. J. Physiol. 25, C226–233.

    Google Scholar 

  70. Boat, T. F. and Dearborn, D. G. (1984),Cystic Fibrosis (Taussig, L. M., ed.), Thieme-Stratton Inc., New York, pp. 25–84.

    Google Scholar 

  71. Widdicombe, J. H. (in press), Ion transport by airway epithelia (The Lung Scientific Fdn.), Raven, New York.

  72. Taussig, L. M., Landau, L. I., and Marks, M. I. (1984),Cystic Fibrosis (Taussig, L. M., ed.), Thieme-Stratton Inc., New York, pp. 115–175.

    Google Scholar 

  73. Rubin, B. K. (1988),Clin. Chest Med. 9, 657–668.

    PubMed  CAS  Google Scholar 

  74. Rossman, C. M. and Newhouse, M. T. (1988),Ped. Pulmon. 5, 36–50.

    Article  CAS  Google Scholar 

  75. Govan, J. R. W. (1975),J. Med. Microbiol. 8, 513–522.

    Article  PubMed  CAS  Google Scholar 

  76. Joris, L. and Quinton, P. (1987),Med. Sci. Res. 15, 855–856.

    CAS  Google Scholar 

  77. Wood, R. E. (1984),Cystic Fibrosis (Taussig, L. M., ed.), Thieme-Stratton Inc., New York, pp. 434–460.

    Google Scholar 

  78. Estivill, X., Farrall, M., Scambler, P. J., Bell, G. M., Hawley, K. M. F., Lench, N. J., Bates, G. P., Kruyer, H. C., Frederick, P. A., Stanier, P., Watson, E. K., Williamson, R., and Wainwright, B. J. (1987),Nature 326, 840–845.

    Article  PubMed  CAS  Google Scholar 

  79. Gristina, A. G., Oga, M., Webb, L. X., and Hobgood, C. D. (1985),Science 228, 990–993.

    Article  PubMed  CAS  Google Scholar 

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Wine, J.J. Basic aspects of cystic fibrosis. Clinical Reviews in Allergy 9, 1–28 (1991). https://doi.org/10.1007/BF02914532

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