The management of hereditary angioedema


Our experience in managing 120 cases of hereditary angioedema is reported. Forty-two severe episodes of mucous or subcutaneous edema were successfully managed using CI-INH concentrate. A prophylactic treatment was done with two classes of drugs: antifibrinolytic agents (tranexamic acid) and 17α-alkylated androgen derivatives.

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Correspondence to Angelo Agostoni.

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Agostoni, A. The management of hereditary angioedema. La Ricerca Clin. Lab. 13, 55–59 (1983).

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  • CI-esterase inhibitor
  • CI-INH concentrate
  • Hereditary angiocedema