Summary
In a 17 year-old male patient with Rotor’s syndrome, hepatic glutathione S-transferase activity toward 1-chloro-2,4-dinitrobenzene reduced to about 0.2% of the mean activity of patients with other diseases. The activities toward sulfobromophthalein and l,2-dichloro-4-nitrobenzene were low (44% and 47%, respectively, of those of controls), but basically present. Bilirubin UDP-glucuronyltransferase activity in this Rotor’s syndrome case was in the normal range.
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Adachi, Y., Yamamoto, T. Partial defect in hepatic glutathione S-transferase activity in a case of Rotor’s syndrome. Gastroenterol Jpn 22, 34–38 (1987). https://doi.org/10.1007/BF02806332
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DOI: https://doi.org/10.1007/BF02806332